ICD-10 Code for Syndrome
The ICD-10-CM 2027 alphabetic index lists syndrome with the subterms below. More specific codes depend on the details documented, as listed in the official index (717 codes, 657 billable).
Index entries for Syndrome
- 4H –
G11.5 - 5q minus NOS –
D46.C - 22q13.3 deletion –
Q93.52 - 48,XXXX –
Q97.1 - 49,XXXXX –
Q97.1 - abdominal
- abnormal innervation –
H02.519 - abstinence, neonatal –
P96.1 - acid pulmonary aspiration, obstetric –
O74.0 - acquired immunodeficiency – see Human, immunodeficiency virus (HIV) disease
- activated phosphoinositide 3-kinase delta syndrome [APDS] –
D81.82 - acute abdominal –
R10.0 - acute respiratory distress (adult) (child) –
J80- idiopathic –
J84.114
- idiopathic –
- Adair-Dighton –
Q78.0 - Adams-Stokes (-Morgagni) –
I45.9 - adiposogenital –
E23.6 - adrenal
- adrenocortical – see Cushing's, syndrome
- adrenogenital –
E25.9- congenital, associated with enzyme deficiency –
E25.0
- congenital, associated with enzyme deficiency –
- afferent loop NEC –
K91.89 - Aicardi-Goutières –
E79.81 - Alagille (-Watson) –
Q44.71 - alcohol withdrawal (without convulsions) – see Dependence, alcohol, with, withdrawal
- Alder's –
D72.0 - Aldrich (-Wiskott) –
D82.0 - alien hand –
R41.4 - Alpha-gal –
Z91.014 - Alport –
Q87.81 - alveolar hypoventilation –
E66.2 - alveolocapillary block –
J84.10 - amnesic, amnestic (confabulatory) (due to) – see Disorder, amnesic
- amyostatic (Wilson's disease) –
E83.01 - androgen insensitivity –
E34.50 - androgen resistance –
E34.50– see also Syndrome, androgen insensitivity - Angelman –
Q93.51 - anginal – see Angina
- ankyloglossia superior –
Q38.1 - anterior
- antibody deficiency –
D80.9 - anticardiolipin (-antibody) –
D68.61 - antidepressant discontinuation –
T43.205(header) - antiphospholipid (-antibody) –
D68.61 - aortic
- aortomesenteric duodenum occlusion –
K31.5 - apical ballooning (transient left ventricular) –
I51.81 - arcuate ligament –
I77.4 - argentaffin, argintaffinoma –
E34.09 - Arnold-Chiari – see Arnold-Chiari disease
- Arrillaga-Ayerza –
I27.0 - arterial tortuosity –
Q87.82 - arteriovenous steal –
T82.898-(header) - Asherman's –
N85.6 - aspiration, of newborn – see Aspiration, by substance, with pneumonia
- meconium –
P24.01
- meconium –
- ataxia-telangiectasia –
G11.3 - auriculotemporal –
G50.8 - autoerythrocyte sensitization (Gardner-Diamond) –
D69.2 - autoimmune polyglandular –
E31.0 - autoimmune lymphoproliferative [ALPS] –
D89.82 - autoinflammatory –
M04.9- specified type NEC –
M04.8
- specified type NEC –
- autosomal – see Abnormal, autosomes
- Avellis' –
G46.8 - Axenfeld-Rieger –
Q13.81 - Ayerza (-Arrillaga) –
I27.0 - Babinski-Nageotte –
G83.89 - Bakwin-Krida –
Q78.5 - Bardet-Biedl –
Q87.83 - bare lymphocyte –
D81.6 - Barré-Guillain –
G61.0 - Barré-Liéou –
M53.0 - Barrett's – see Barrett's, esophagus
- Barsony-Polgar –
K22.4 - Barsony-Teschendorf –
K22.4 - Barth –
E78.71 - Bartter's –
E26.81 - basal cell nevus –
Q87.89 - Basedow's –
E05.00- with thyroid storm –
E05.01
- with thyroid storm –
- basilar artery –
G45.0 - Batten-Steinert –
G71.11 - battered
- baby or child – see Maltreatment, child, physical abuse
- spouse – see Maltreatment, adult, physical abuse
- Beals –
Q87.40 - Beau's –
I51.5 - Beck's –
I65.8 - Benedikt's –
G46.3 - Béquez César (-Steinbrinck-Chédiak-Higashi) –
E70.330 - Berardinelli-Siep –
E88.12 - Bernhardt-Roth – see Meralgia paresthetica
- Bernheim's – see Failure, heart, right
- big spleen –
D73.1 - bilateral polycystic ovarian –
E28.2 - Bing-Horton's – see Horton's headache
- Birt-Hogg-Dube syndrome –
Q87.89 - Björck (-Thorsen) –
E34.09 - black
- lung –
J60 - widow spider bite – see Toxicity, venom, spider, black widow
- lung –
- Blackfan-Diamond –
D61.01 - Blau –
M04.8 - blind loop –
K90.2 - blue sclera –
Q78.0 - blue toe –
I75.02-(header) - Boder-Sedgewick –
G11.3 - Boerhaave's –
K22.3 - Borjeson Forssman Lehmann –
Q89.89 - Bouillaud's –
I01.9 - Bourneville (-Pringle) –
Q85.1 - Bouveret (-Hoffman) –
I47.9 - brachial plexus –
G54.0 - bradycardia-tachycardia –
I49.5 - brain (nonpsychotic) –
F09 - brain stem stroke –
G46.3 - Brandt's (acrodermatitis enteropathica) –
E83.2 - BRCA1-cancer predisposition –
QA1.790 - BRCA2-cancer predisposition –
QA1.791 - broad ligament laceration –
N83.8 - Brock's –
J98.11 - bronchiolitis obliterans –
J44.81– see also Bronchiolitis, obliterative - bronze baby –
P83.88 - Brown-Sequard –
G83.81 - Brugada –
I49.81 - bubbly lung –
P27.0 - Buchem's –
M85.2 - Budd-Chiari –
I82.0 - bulbar (progressive) –
G12.22 - Bürger-Grütz –
E78.3 - Burke's –
K86.89 - Burnett's (milk-alkali) –
E83.52 - burning feet –
E53.9 - Bywaters' –
T79.5(header) - Call-Fleming –
I67.841 - cannabinoid hyperemesis –
R11.16 - cannabis hyperemesis –
R11.16 - carbohydrate-deficient glycoprotein (CDGS) –
E77.8 - carcinogenic thrombophlebitis –
I82.1 - carcinoid –
E34.00 - cardiac asthma –
I50.1 - cardiacos negros –
I27.0 - cardiofaciocutaneous –
Q87.89 - cardiopulmonary-obesity –
E66.2 - cardiorenal Note: – see Failure, heart; also see Failure, renal
- cardiorespiratory distress (idiopathic) –
P22.0 - cardiovascular renal Note: – see Failure, heart; also see Failure, renal
- carotid
- carpal tunnel –
G56.0-(header) - Cassidy (-Scholte) –
E34.09 - cat cry –
Q93.4 - cat eye –
Q92.8 - cauda equina –
G83.4 - causalgia – see Causalgia
- celiac –
K90.0 - central pain –
G89.0 - cerebellar
- cerebellomedullary malformation – see Spina bifida
- cerebral
- cervical (root) –
M53.1- disc – see Disorder, disc, cervical, with neuritis
- fusion –
Q76.1 - posterior, sympathicus –
M53.0 - rib –
Q76.5 - sympathetic paralysis –
G90.2
- cervicobrachial (diffuse) –
M53.1 - cervicocranial –
M53.0 - cervicodorsal outlet –
G54.2 - cervicothoracic outlet –
G54.0– see also Syndrome, thoracic outlet - Céstan (-Raymond) –
I65.8 - Charcot's (angina cruris) (intermittent claudication) –
I73.9 - Charcot-Weiss-Baker –
G90.09 - CHARGE –
Q89.89 - Chédiak-Higashi (-Steinbrinck) –
E70.330 - chest wall –
R07.1 - Chiari's (hepatic vein thrombosis) –
I82.0 - Chilaiditi's –
Q43.3 - child maltreatment – see Maltreatment, child
- chondrocostal junction –
M94.0 - chondroectodermal dysplasia –
Q77.6 - chromosome 4 short arm deletion –
Q93.3 - chromosome 5 short arm deletion –
Q93.4 - chronic
- Churg-Strauss –
M30.1 - Clarke-Hadfield –
K86.89 - Clerambault's automatism –
G93.89 - clinically isolated –
G37.9 - Clouston's (hidrotic ectodermal dysplasia) –
Q82.4 - clumsiness, clumsy child –
F82 - cluster headache –
G44.009 - Coffin-Lowry –
Q89.89 - cold injury (newborn) –
P80.0 - combined immunity deficiency –
D81.9 - compartment (deep) (posterior) (traumatic) –
T79.A0(header)- abdomen –
T79.A3(header) - lower extremity (hip, buttock, thigh, leg, foot, toes) –
T79.A2(header) - nontraumatic
- postprocedural – see Syndrome, compartment, nontraumatic
- specified site NEC –
T79.A9(header) - upper extremity (shoulder, arm, forearm, wrist, hand, fingers) –
T79.A1(header)
- abdomen –
- complex regional pain – see Syndrome, pain, complex regional
- compression –
T79.5(header) - concussion –
F07.81 - congenital
- congestion-fibrosis (pelvic) –
N94.89 - congestive dysmenorrhea –
N94.6 - Conn's –
E26.01 - connective tissue –
M35.9- overlap NEC –
M35.1
- overlap NEC –
- conus medullaris –
G95.81 - cord
- coronary
- Costen's (complex) –
M26.69 - costochondral junction –
M94.0 - costoclavicular –
G54.0 - costovertebral –
E22.0 - Cowden
- craniovertebral –
M53.0 - Creutzfeldt-Jakob – see Creutzfeldt-Jakob disease or syndrome
- cri-du-chat –
Q93.4 - crib death –
R99 - cricopharyngeal – see Dysphagia
- croup –
J05.0 - CRPS I – see Syndrome, pain, complex regional I
- crush –
T79.5(header) - CTNNB1 –
Q87.88 - cubital tunnel – see Lesion, nerve, ulnar
- Curschmann (-Batten) (-Steinert) –
G71.11 - Cushing's –
E24.9 - cryopyrin-associated periodic –
M04.2 - cryptophthalmos –
Q87.0 - cystic duct stump –
K91.5 - cytokine release –
D89.839 - Dana-Putnam –
D51.0 - Danbolt (-Cross) (acrodermatitis enteropathica) –
E83.2 - Dandy-Walker –
Q03.1- with spina bifida –
Q07.01
- with spina bifida –
- Danlos' –
Q79.60– see also Syndrome, Ehlers-Danlos - defibrination – see also Fibrinolysis
- with
- antepartum hemorrhage – see Hemorrhage, antepartum, with coagulation defect
- intrapartum hemorrhage – see Hemorrhage, complicating, delivery
- newborn –
P60 - postpartum –
O72.3
- with
- Degos' –
I77.89 - Déjérine-Roussy –
G89.0 - delayed sleep phase –
G47.21 - demyelinating –
G37.9 - dependence – see F10-F19 with fourth character .2
- depersonalization (-derealization) –
F48.1 - De Quervain –
E34.51 - de Toni-Fanconi (-Debré) –
E72.09- with cystinosis –
E72.04
- with cystinosis –
- de Vivo syndrome –
E74.810 - diabetes mellitus-hypertension-nephrosis – see Diabetes, nephrosis
- diabetes mellitus in newborn infant –
P70.2 - diabetes-nephrosis – see Diabetes, nephrosis
- diabetic amyotrophy – see Diabetes, amyotrophy
- dialysis associated steal –
T82.898-(header) - Diamond-Blackfan –
D61.01 - Diamond-Gardener –
D69.2 - DIC (diffuse or disseminated intravascular coagulopathy) –
D65 - di George's –
D82.1 - Dighton's –
Q78.0 - disequilibrium –
E87.8 - Döhle body-panmyelopathic –
D72.0 - dorsolateral medullary –
G46.4 - double athetosis –
G80.3 - Down –
Q90.9– see also Down syndrome - Dravet (intractable) –
G40.834 - Dresbach's (elliptocytosis) –
D58.1 - DRESS (drug rash with eosinophilia and systemic symptoms) –
D72.12 - Dressler's (postmyocardial infarction) –
I24.1- postcardiotomy –
I97.0
- postcardiotomy –
- drug rash with eosinophilia and systemic symptoms (DRESS) –
D72.12 - drug withdrawal, infant of dependent mother –
P96.1 - dry eye –
H04.12-(header) - due to abnormality
- dumping (postgastrectomy) –
K91.1- nonsurgical –
K31.89
- nonsurgical –
- Dupré's (meningism) –
R29.1 - dysmetabolic X –
E88.810 - dyspraxia, developmental –
F82 - Eagle-Barrett –
Q79.4 - Eaton-Lambert – see Syndrome, Lambert-Eaton
- Ebstein's –
Q22.5 - ectopic ACTH –
E24.3 - eczema-thrombocytopenia –
D82.0 - Eddowes' –
Q78.0 - effort (psychogenic) –
F45.8 - Eisenmenger's –
I27.83 - Ehlers-Danlos –
Q79.60 - Ekman's –
Q78.0 - electric feet –
E53.8 - Ellis-van Creveld –
Q77.6 - empty nest –
Z60.0 - endocrine-hypertensive –
E27.0 - entrapment – see Neuropathy, entrapment
- eosinophilia-myalgia –
M35.89 - epileptic – see also Epilepsy, by type
- Erdheim-Chester (ECD) –
E88.89 - Erdheim's –
E22.0 - erythrocyte fragmentation –
D59.4 - Evans –
D69.41 - exhaustion –
F48.8 - extrapyramidal –
G25.9- specified NEC –
G25.89
- specified NEC –
- eye retraction – see Strabismus
- eyelid-malar-mandible –
Q87.0 - Faber's –
D50.9 - facet –
M47.89-(header) - facet joint –
M47.819– see also Spondylosis - facial pain, paroxysmal –
G50.0 - Fallot's –
Q21.3 - familial cancer
- with
- pathogenic BRCA1 mutation –
QA1.790 - pathogenic BRCA2 mutation –
QA1.791
- pathogenic BRCA1 mutation –
- with
- familial cold autoinflammatory –
M04.2 - familial eczema-thrombocytopenia (Wiskott-Aldrich) –
D82.0 - Fanconi (-de Toni) (-Debré) –
E72.09- with cystinosis –
E72.04
- with cystinosis –
- fatigue
- faulty bowel habit –
K59.39 - Feil-Klippel (brevicollis) –
Q76.1 - Felty's – see Felty's syndrome
- fertile eunuch –
E23.0 - fetal
- Fiedler's –
I40.1 - first arch –
Q87.0 - fish odor –
E72.89 - Fisher's –
G61.0 - Fitzhugh-Curtis
- Fitz's –
K85.80– see also Pancreatitis, acute - Flajani (-Basedow) –
E05.00- with thyroid storm –
E05.01
- with thyroid storm –
- flatback – see Flatback syndrome
- floppy
- flush –
E34.09 - Foix-Alajouanine –
G95.19 - Fong's –
Q87.2 - food protein-induced enterocolitis (FPIES) –
K52.21 - foramen magnum –
G93.5 - Foster-Kennedy –
H47.14-(header) - Foville's (peduncular) –
G46.3 - FOXG1 –
QA0.0151 - fragile X –
Q99.2 - Franceschetti –
Q75.4 - Frey's
- Friderichsen-Waterhouse –
A39.1 - Froin's –
G95.89 - frontal lobe –
F07.0 - Fukuhara –
E88.49 - functional
- Gaisböck's –
D75.1 - ganglion (basal ganglia brain) –
G25.9- geniculi –
G51.1
- geniculi –
- Gardner-Diamond –
D69.2 - gastroesophageal
- gastrojejunal loop obstruction –
K91.89 - Gee-Herter-Heubner –
K90.0 - Gelineau's –
G47.419- with cataplexy –
G47.411
- with cataplexy –
- genito-anorectal –
A55 - Gerstmann-Sträussler-Scheinker (GSS) –
A81.82 - Gianotti-Crosti –
L44.4 - giant platelet (Bernard-Soulier) –
D69.19 - Gilles de la Tourette's –
F95.2 - Glass –
Q87.89 - Gleich's –
D72.118 - goiter-deafness –
E07.1 - Goldberg –
Q89.89 - Goldberg-Maxwell –
E34.51 - Good's –
D83.8 - Gopalan's (burning feet) –
E53.8 - Gorlin's –
Q87.89 - Gougerot-Blum –
L81.7 - Gouley's –
I31.1 - Gower's –
R55 - gray or grey (newborn) –
P93.0- platelet –
D69.19
- platelet –
- Gubler-Millard –
G46.3 - Guillain-Barré (-Strohl) –
G61.0 - Gulf war –
T75.830(header) - gustatory sweating –
G50.8 - Hadfield-Clarke –
K86.89 - hair tourniquet – see Constriction, external, by site
- Hamman's –
J98.19 - hand-foot –
L27.1 - hand-shoulder –
G90.89 - hantavirus (cardio)-pulmonary (HPS) (HCPS) –
B33.4 - Hao-Fountain (HAFOUS) –
Q87.87 - happy puppet –
Q93.51 - Harada's –
H30.81-(header) - Hayem-Faber –
D50.9 - headache NEC –
G44.89- complicated NEC –
G44.59
- complicated NEC –
- Heberden's –
I20.89 - Hedinger's –
E34.01 - Hegglin's –
D72.0 - HELLP (hemolysis, elevated liver enzymes and low platelet count) –
O14.2-(header) - hemolytic-uremic –
D59.30 - hemophagocytic, infection-associated –
D76.2 - Henoch-Schönlein –
D69.0 - hepatic flexure –
K59.89 - hepatopulmonary –
K76.81 - hepatorenal –
K76.7 - hepatourologic –
K76.7 - hereditary alpha tryptasemia –
D89.44 - hereditary breast and ovarian cancer
- with
- pathogenic BRCA1 mutation –
QA1.790 - pathogenic BRCA2 mutation –
QA1.791
- pathogenic BRCA1 mutation –
- with
- Herter (-Gee) (nontropical sprue) –
K90.0 - Heubner-Herter –
K90.0 - Heyd's –
K76.7 - Hilger's –
G90.09 - histamine-like (fish poisoning) – see Poisoning, fish
- histiocytic –
D76.3 - histiocytosis NEC –
D76.3 - HIV infection, acute –
B20 - Hoffmann-Werdnig –
G12.0 - Hollander-Simons –
E88.19 - Hoppe-Goldflam –
G70.00 - Horner's –
G90.2 - hungry bone –
E83.81 - hunterian glossitis –
D51.0 - Hunt's (herpetic geniculate ganglionitis) (neuralgia) –
B02.21- dyssynergia cerebellaris myoclonica –
G11.19
- dyssynergia cerebellaris myoclonica –
- Hutchinson's triad –
A50.53 - hyperabduction –
G54.0 - hyperammonemia-hyperornithinemia-homocitrullinemia –
E72.4 - hypereosinophilic (HES) –
D72.119 - hyperimmunoglobulin D –
M04.1 - hyperimmunoglobulin E (IgE) –
D82.4 - hyperkalemic –
E87.5 - hyperkinetic – see Hyperkinesia
- hypermobility –
M35.7 - hypernatremia –
E87.0 - hyperosmolarity (see also, Diabetes, by type, with hyperosmolarity) –
E87.0 - hyperperfusion –
G97.82 - hypersplenic –
D73.1 - hypertransfusion, newborn –
P61.1 - hyperventilation –
F45.8 - hyperviscosity ( of serum)
- hypoglycemic (familial) (neonatal) –
E16.2 - hypokalemic –
E87.6 - hyponatremic –
E87.1 - hypopituitarism –
E23.0 - hypoplastic left-heart –
Q23.4 - hypopotassemia –
E87.6 - hyposmolality –
E87.1 - hypotension, maternal –
O26.5-(header) - hypothenar hammer –
I73.89 - hypoventilation, obesity (OHS) –
E66.2 - ICF (intravascular coagulation-fibrinolysis) –
D65 - idiopathic
- iliotibial band –
M76.3-(header) - immobility, immobilization (paraplegic) –
M62.3 - immune effector cell-associated neurotoxicity (ICANS) –
G92.00 - immune reconstitution –
D89.3 - immune reconstitution inflammatory [IRIS] –
D89.3 - immunity deficiency, combined –
D81.9 - immunodeficiency
- acquired – see Human, immunodeficiency virus (HIV) disease
- combined –
D81.9
- impending coronary –
I20.0 - impingement, shoulder –
M75.4-(header) - inappropriate secretion of antidiuretic hormone –
E22.2 - infant
- infantilism (pituitary) –
E23.0 - inferior vena cava –
I87.1 - inherited neoplasm predisposition syndrome of multiple systems, specified NEC –
QA1.798 - inspissated bile (newborn) –
P59.1 - institutional (childhood) –
F94.2 - insufficient sleep –
F51.12 - insulin resistance
- intermediate coronary (artery) –
I20.0 - interspinous ligament – see Spondylopathy, specified NEC
- intestinal
- intravascular coagulation-fibrinolysis (ICF) –
D65 - iodine-deficiency, congenital –
E00.9 - IRDS (idiopathic respiratory distress, newborn) –
P22.0 - irritable
- ischemic
- IVC (intravascular coagulopathy) –
D65 - Ivemark's –
Q89.01 - Jaccoud's – see Arthropathy, postrheumatic, chronic
- Jackson's –
G83.89 - Jakob-Creutzfeldt – see Creutzfeldt-Jakob disease or syndrome
- jaw-winking –
Q07.8 - Jervell-Lange-Nielsen –
I45.81 - jet lag –
G47.25 - Job's –
D71.8 - Joseph-Diamond-Blackfan –
D61.01 - jugular foramen –
G52.7 - Kabuki (type 1, due to KMT2D mutation) (type 2, due to KDM6A mutation) –
Q89.81 - Kanner's (autism) –
F84.0 - Kartagener's –
Q89.3 - Kelly's –
D50.1 - Kimmelstiel-Wilson – see Diabetes, specified type, with Kimmelstiel-Wilson disease
- Kleefstra –
Q87.86 - Klein (e) –
G47.13 - Klippel-Feil (brevicollis) –
Q76.1 - Köhler-Pellegrini-Stieda – see Bursitis, tibial collateral
- König's –
K59.89 - Korsakoff (-Wernicke) (nonalcoholic) –
F04 - Kostmann's –
D70.0 - Krabbe's congenital muscle hypoplasia –
Q79.8 - labyrinthine
- lacunar NEC –
G46.7 - Lambert-Eaton –
G70.80 - Landau-Kleffner – see Epilepsy, specified NEC
- Larsen's –
Q74.8 - Lassueur Graham-Little Piccardi –
L66.19 - lateral
- Launois' –
E22.0 - Laurence-Moon –
Q87.84 - Lawrence –
E88.12 - lazy
- Lemierre –
I80.8 - Lennox-Gastaut –
G40.812 - lenticular, progressive –
E83.01 - Leopold-Levi's –
E05.90 - Lev's –
I44.2 - Li-Fraumeni –
QA1.792 - Lichtheim's –
D51.0 - Lightwood's –
N25.89 - Lignac (de Toni) (-Fanconi) (-Debré) –
E72.09- with cystinosis –
E72.04
- with cystinosis –
- Likoff's –
I20.89 - limbic epilepsy personality –
F07.0 - liver-kidney –
K76.7 - lobotomy –
F07.0 - Loeys-Dietz –
Q87.A - Löffler's –
J82.89 - long arm 18 or 21 deletion –
Q93.89 - long QT –
I45.81 - Louis-Barré –
G11.3 - low
- lower radicular, newborn (birth injury) –
P14.8 - Luetscher's (dehydration) –
E86.0 - Lupus anticoagulant –
D68.62 - Lutembacher's –
Q21.19 - Lynch (due to EPCAM) (due to MLH1) (due to MSH2) (due to MSH6) (due to PMS2) –
QA1.71 - macrophage activation –
D76.1- due to infection –
D76.2
- due to infection –
- magnesium-deficiency –
R29.0 - Majeed –
M04.8 - Mal de Debarquement –
R42 - malabsorption –
K90.9- postsurgical –
K91.2
- postsurgical –
- malformation, congenital, due to
- malignant
- Mallory-Weiss –
K22.6 - mandibulofacial dysostosis –
Q75.4 - manic-depressive – see Disorder, bipolar
- maple-syrup-urine –
E71.0 - Marable's –
I77.4 - Marfan –
Q87.40 - Marie's (acromegaly) –
E22.0 - mast cell activation – see Activation, mast cell
- maternal hypotension – see Syndrome, hypotension, maternal
- May (-Hegglin) –
D72.0 - McArdle (-Schmidt) (-Pearson) –
E74.04 - McQuarrie's –
E16.2 - meconium plug (newborn) –
P76.0 - MED13L (mediator complex subunit 13L) –
Q87.85 - median arcuate ligament –
I77.4 - mediator complex subunit 13L (MED13L) –
Q87.85 - Meekeren-Ehlers-Danlos –
Q79.6(header) - megavitamin-B6 –
E67.2 - Meige –
G24.4 - MELAS –
E88.41 - Mendelson's –
O74.0 - MERRF (myoclonic epilepsy associated with ragged-red fibers) –
E88.42 - mesenteric
- metabolic –
E88.810 - metastatic carcinoid –
E34.00 - micrognathia-glossoptosis –
Q87.0 - midbrain NEC –
G93.89 - middle lobe (lung) –
J98.19 - middle radicular –
G54.0 - migraine –
G43.909-– see also Migraine - Mikulicz' –
K11.8 - milk-alkali –
E83.52 - Millard-Gubler –
G46.3 - Miller-Dieker –
Q93.88 - Miller-Fisher –
G61.0 - Minkowski-Chauffard –
D58.0 - Mirizzi's –
K83.1 - MNGIE (Mitochondrial Neurogastrointestinal Encephalopathy) –
E88.49 - Möbius, ophthalmoplegic migraine – see Migraine, ophthalmoplegic
- monofixation –
H50.42 - Morel-Moore –
M85.2 - Morel-Morgagni –
M85.2 - Morgagni (-Morel) (-Stewart) –
M85.2 - Morgagni-Adams-Stokes –
I45.9 - Muckle-Wells –
M04.2 - mucocutaneous lymph node (acute febrile) (MCLS) –
M30.3 - multiple endocrine neoplasia (MEN) – see Neoplasia, endocrine, multiple (MEN)
- multiple operations – see Disorder, factitious
- multisystem inflammatory (in adults) (in children) –
M35.81 - Mounier-Kuhn –
Q32.4 - myasthenic –
G70.9 - myelodysplastic –
D46.9 - myeloid hypereosinophilic –
D72.118 - myelopathic pain –
G89.0 - myeloproliferative (chronic) –
D47.1 - myofascial pain –
M79.18 - Naffziger's –
G54.0 - nail patella –
Q87.2 - NARP (Neuropathy, Ataxia and Retinitis pigmentosa) –
E88.49 - neonatal abstinence –
P96.1 - nephritic – see also Nephritis
- nephrotic (congenital) –
N04.9– see also Nephrosis - neurologic neglect –
R41.4 - Nezelof's –
D81.4 - Niikawa-Kuroki –
Q89.81 - Nonne-Milroy-Meige –
Q82.0 - Nothnagel's vasomotor acroparesthesia –
I73.89 - obesity hypoventilation (OHS) –
E66.2 - obliterans
- bronchiolitis –
J44.81– see also Bronchiolitis, obliterative
- bronchiolitis –
- oculomotor –
H51.9 - Ogilvie –
K59.81 - Oliver-McFarlane –
Q87.89 - ophthalmoplegia-cerebellar ataxia – see Strabismus, paralytic, third nerve
- oral allergy –
T78.19(header) - oral-facial-digital –
Q87.0 - organic
- Ormond's –
N13.5 - oro-facial-digital –
Q87.0 - os trigonum –
Q68.8 - Osler-Weber-Rendu –
I78.0 - osteoporosis-osteomalacia –
M83.8 - Osterreicher-Turner –
Q87.2 - otolith
- oto-palatal-digital –
Q87.0 - outlet (thoracic) –
G54.0– see also Syndrome, thoracic outlet - ovary
- Owren's –
D68.2 - Paget-Schroetter –
I82.890 - pain – see also Pain
- painful
- paralysis agitans – see Parkinsonism
- paralytic –
G83.9- specified NEC –
G83.89
- specified NEC –
- Parinaud's –
H51.0 - parkinsonian – see Parkinsonism
- Parkinson's – see Parkinsonism
- paroxysmal facial pain –
G50.0 - Parry's –
E05.00- with thyroid storm –
E05.01
- with thyroid storm –
- Parsonage (-Aldren) –
G54.5 - patella clunk –
M25.86-(header) - Paterson (-Brown) (-Kelly) –
D50.1 - pectoral girdle –
I77.89 - pectoralis minor –
I77.89 - pediatric acute-onset neuropsychiatric (PANS) –
D89.89 - pediatric autoimmune neuropsychiatric disorders associated with streptococcal infections (PANDAS) –
D89.89 - pediatric inflammatory multisystem –
M35.81 - Pelger-Huet –
D72.0 - pellagra-cerebellar ataxia-renal aminoaciduria –
E72.02 - pellagroid –
E52 - Pellegrini-Stieda – see Bursitis, tibial collateral
- pelvic congestion-fibrosis, female –
N94.89 - penta X –
Q97.1 - peptic ulcer – see Ulcer, peptic
- perabduction –
I77.89 - periodic fever –
M04.1 - periodic fever, aphthous stomatitis, pharyngitis, and adenopathy [PFAPA] –
M04.8 - periodic headache, in adults and children – see Headache, periodic syndromes in adults and children
- periurethral fibrosis –
N13.5 - Peutz-Jeghers –
Q85.89 - phantom limb (without pain) –
G54.7- with pain –
G54.6
- with pain –
- pharyngeal pouch –
D82.1 - Phelan-McDermid –
Q93.52 - Pick's – see Disease, Pick's
- Pickwickian –
E66.2 - PIE (pulmonary infiltration with eosinophilia) –
J82.89– see also Eosinophilia, pulmonary - pigmentary pallidal degeneration (progressive) –
G23.0 - pineal –
E34.8 - pituitary –
E22.0 - plantar fascia –
M72.2-(header) - placental transfusion – see Pregnancy, complicated by, placental transfusion syndromes
- plateau iris (post-iridectomy) (postprocedural) –
H21.82 - Plummer-Vinson –
D50.1 - pluricarential of infancy –
E40 - plurideficiency –
E40 - pluriglandular (compensatory) –
E31.8- autoimmune –
E31.0
- autoimmune –
- pneumatic hammer –
T75.21(header) - polyangiitis overlap –
M30.8 - polycarential of infancy –
E40 - polyglandular –
E31.8- autoimmune –
E31.0
- autoimmune –
- polysplenia –
Q89.09 - pontine NEC –
G93.89 - popliteal
- postbacterial fatigue –
G93.39 - postcardiac injury
- postcardiotomy –
I97.0 - post chemoembolization - code to associated conditions
- postcholecystectomy –
K91.5 - postcommissurotomy –
I97.0 - postconcussional –
F07.81 - postcontusional –
F07.81 - post-COVID (-19) –
U09.9 - postencephalitic –
F07.89 - post endometrial ablation –
N99.85 - post-polypectomy coagulation –
K91.89 - posterior
- postgastrectomy (dumping) –
K91.1 - postgastric surgery –
K91.1 - postinfarction –
I24.1 - postinfectious fatigue –
G93.39 - postlaminectomy NEC –
M96.1 - postleukotomy –
F07.0 - postmastectomy lymphedema –
I97.2 - postmyocardial infarction –
I24.1 - postoperative NEC –
T81.9(header)- blind loop –
K90.2
- blind loop –
- postpartum panhypopituitary (Sheehan) –
E23.0 - postpolio (myelitic) –
G14 - postthrombotic –
I87.009 - postural
- postvagotomy –
K91.1 - postvalvulotomy –
I97.0 - postviral NEC –
G93.31- fatigue –
G93.31
- fatigue –
- Potain's –
K31.0 - potassium intoxication –
E87.5 - Prader-Willi –
Q87.11 - Prader-Willi-like –
Q87.19 - precerebral artery (multiple) (bilateral) –
G45.2 - preinfarction –
I20.0 - preleukemic –
D46.9 - premature senility –
E34.8 - premenstrual dysphoric –
F32.81 - premenstrual tension –
N94.3 - Prinzmetal-Massumi –
R07.1 - prune belly –
Q79.4 - pseudocarpal tunnel (sublimis) – see Syndrome, carpal tunnel
- pseudoparalytica –
G70.00 - pseudo -Turner's –
Q87.19 - psycho-organic (nonpsychotic severity) –
F07.9 - PTEN (hamartoma) –
Q85.81 - pulmonary
- pure
- Putnam-Dana –
D51.0 - pyogenic arthritis, pyoderma gangrenosum, and acne [PAPA] –
M04.8 - pyramidopallidonigral –
G20.C - pyriformis – see Lesion, nerve, sciatic
- QT interval prolongation –
I45.81 - radicular NEC – see Radiculopathy
- upper limbs, newborn (birth injury) –
P14.3
- upper limbs, newborn (birth injury) –
- rapid time-zone change –
G47.25 - Rasmussen –
G04.81 - Raymond (-Céstan) –
I65.8 - Raynaud's –
I73.00- with gangrene –
I73.01
- with gangrene –
- RDS (respiratory distress syndrome, newborn) –
P22.0 - reactive airways dysfunction –
J68.3 - Refsum's –
G60.1 - Reifenstein –
E34.52 - renal glomerulohyalinosis-diabetic – see Diabetes, nephrosis
- Rendu-Osler-Weber –
I78.0 - residual ovary –
N99.83 - resistant ovary –
E28.39 - respiratory
- restless legs –
G25.81 - restrictive allograft –
J4A.0 - retinoblastoma (familial) –
C69.2(header) - retroperitoneal fibrosis –
K68.2 - retroviral seroconversion (acute) –
Z21 - Reye's –
G93.7 - Richter – see Leukemia, chronic lymphocytic, B-cell type
- Ridley's –
I50.1 - right
- heart, hypoplastic –
Q22.6 - ventricular obstruction – see Failure, heart, right
- heart, hypoplastic –
- Romano-Ward (prolonged QT interval) –
I45.81 - rotator cuff, shoulder –
M75.10-(header) – see also Tear, rotator cuff - Rotes Quérol – see Hyperostosis, ankylosing
- Roth – see Meralgia paresthetica
- rubella (congenital) –
P35.0 - Ruvalcaba-Myhre-Smith –
E71.440 - Rytand-Lipsitch –
I44.2 - salt
- salt-losing –
N28.89 - SATB2-associated –
Q87.89 - Scaglietti-Dagnini –
E22.0 - scalenus anticus (anterior) –
G54.0 - scapulocostal – see Mononeuropathy, upper limb, specified site NEC
- scapuloperoneal –
G71.09 - schizophrenic, of childhood NEC –
F20.9 - Schnitzler –
D47.2 - Scholte's –
E34.09 - Schroeder's –
E27.0 - Schüller-Christian –
C96.5 - Schwachman (-Diamond) –
D61.02 - Schwartz (-Jampel) –
G71.13 - Schwartz-Bartter –
E22.2 - scimitar –
Q26.8 - sclerocystic ovary –
E28.2 - Seitelberger's –
G31.89 - septicemic adrenal hemorrhage –
A39.1 - seroconversion, retroviral (acute) –
Z21 - serotonin –
G90.81 - serous meningitis –
G93.2 - severe acute respiratory (SARS) –
J12.81 - shaken infant –
T74.4(header) - shock (traumatic) –
T79.4(header) - shock-lung –
J80 - Shone's - code to specific anomalies
- short
- shoulder-hand – see Algoneurodystrophy
- Shwachman (-Diamond) –
D61.02 - sicca – see Syndrome, Sjögren
- sick
- sick-euthyroid –
E07.81 - sideropenic –
D50.1 - Siemens' ectodermal dysplasia –
Q82.4 - Silfversköld's –
Q78.9 - Simons' –
E88.11 - sinus tarsi –
M25.57-(header) - sinusitis-bronchiectasis-situs inversus –
Q89.3 - Sipple's –
E31.22 - sirenomelia –
Q87.2 - Sjögren –
M35.00- with
- central nervous system involvement –
M35.07 - dental involvement –
M35.0C - gastrointestinal involvement –
M35.08 - glomerular disease –
M35.0A - inflammatory arthritis –
M35.05 - keratoconjunctivitis –
M35.01 - lung involvement –
M35.02 - myopathy –
M35.03 - peripheral nervous system involvement –
M35.06 - renal tubular acidosis –
M35.04 - specified organ involvement, NEC –
M35.09 - tubulo-interstitial nephropathy –
M35.04 - vasculitis –
M35.0B
- central nervous system involvement –
- with
- Slocumb's –
E27.0 - slow flow, coronary –
I20.89 - Sluder's –
G44.89 - Smith-Magenis –
Q93.88 - Sneddon-Wilkinson –
L13.1 - Snyder-Robinson –
Q87.89 - Soto's –
Q87.3 - South African cardiomyopathy –
I42.89 - spasmodic
- Spen's –
I45.9 - splenic
- Spurway's –
Q78.0 - staphylococcal scalded skin –
L00 - steal
- Stein-Leventhal –
E28.2 - Stein's –
E28.2 - Stevens-Johnson syndrome –
L51.1- toxic epidermal necrolysis overlap –
L51.3
- toxic epidermal necrolysis overlap –
- Stewart-Morel –
M85.2 - Stickler –
Q89.89 - stiff baby –
Q89.89 - stiff man –
G25.82 - Still-Felty – see Felty's syndrome
- Stokes (-Adams) –
I45.9 - stone heart –
I50.1 - straight back, congenital –
Q76.49 - Sturge-Weber (-Dimitri) –
Q85.89 - subclavian steal –
G45.8 - subcoracoid-pectoralis minor –
G54.0 - subcostal nerve compression –
I77.89 - subphrenic interposition –
Q43.3 - superior
- supine hypotensive (maternal) – see Syndrome, hypotension, maternal
- suprarenal cortical –
E27.0 - supraspinatus –
M75.10-(header) – see also Tear, rotator cuff - Susac –
G93.49 - swallowed blood –
P78.2 - sweat retention –
L74.0 - Swyer –
Q99.1 - Symond's –
G93.2 - sympathetic
- systemic inflammatory response (SIRS), of non-infectious origin (without organ dysfunction) –
R65.10- with acute organ dysfunction –
R65.11
- with acute organ dysfunction –
- tachycardia-bradycardia –
I49.5 - takotsubo –
I51.81 - TAR (thrombocytopenia with absent radius) –
Q87.2 - tarsal tunnel –
G57.5-(header) - teething –
K00.7 - tegmental –
G93.89 - telangiectasic-pigmentation-cataract –
Q82.8 - temporal pyramidal apex – see Otitis, media, suppurative, acute
- temporomandibular joint-pain-dysfunction –
M26.62-(header) - Terry's –
H44.2-(header) – see also Myopia, degenerative - testicular feminization –
E34.51– see also Syndrome, androgen insensitivity - thalamic pain (hyperesthetic) –
G89.0 - thoracic outlet (compression) –
G54.0 - Thorson-Björck –
E34.09 - thrombocytopenia with absent radius (TAR) –
Q87.2 - thrombosis with thrombocytopenia –
D75.84 - thyroid-adrenocortical insufficiency –
E31.0 - tibial
- Tietze's –
M94.0 - time-zone (rapid) –
G47.25 - Toni-Fanconi –
E72.09- with cystinosis –
E72.04
- with cystinosis –
- Touraine's –
Q79.8 - tourniquet – see Constriction, external, by site
- toxic shock –
A48.3 - transient left ventricular apical ballooning –
I51.81 - traumatic vasospastic –
T75.22(header) - Treacher Collins –
Q75.4 - triple X, female –
Q97.0 - trisomy –
Q92.9 - tropical wet feet –
T69.02-(header) - Trousseau's –
I82.1 - tumor lysis (following antineoplastic chemotherapy) (spontaneous) –
E88.3 - tumor necrosis factor receptor associated periodic (TRAPS) –
M04.1 - Twiddler's (due to)
- Unverricht (-Lundborg) – see Epilepsy, generalized, idiopathic
- upward gaze –
H51.8 - uremia, chronic –
N18.9– see also Disease, kidney, chronic - urethral –
N34.3 - urethro-oculo-articular – see Reiter's disease
- urohepatic –
K76.7 - usher –
Q99.819 - vacuoles, E1 ubiquitin-activating enzyme, X-linked, autoinflammatory, somatic (VEXAS) –
M04.3 - vago-hypoglossal –
G52.7 - vanishing twin of one fetus or more –
O31.4-(header) - vascular NEC in cerebrovascular disease –
G46.8 - vasoconstriction, reversible cerebrovascular –
I67.841 - vasomotor –
I73.9 - vasospastic (traumatic) –
T75.22(header) - vasovagal –
R55 - van Buchem's –
M85.2 - van der Hoeve's –
Q78.0 - VATER –
Q87.2 - velo-cardio-facial –
Q93.81 - vena cava (inferior) (superior) (obstruction) –
I87.1 - vertebral
- artery –
G45.0- compression – see Syndrome, anterior, spinal artery, compression
- steal –
G45.0
- artery –
- vertebro-basilar artery –
G45.0 - vertebrogenic (pain) –
M54.89– see also Pain, vertebrogenic - vertiginous – see Disorder, vestibular function
- VEXAS (vacuoles, E1 ubiquitin-activating enzyme, X-linked, autoinflammatory, somatic) –
M04.3 - Vinson-Plummer –
D50.1 - virus –
B34.9 - visceral larva migrans –
B83.0 - visual disorientation –
H53.8 - vitamin B6 deficiency –
E53.1 - vitreal corneal –
H59.01-(header) - vitreous (touch) –
H59.01-(header) - Vogt-Koyanagi –
H20.82-(header) - Volkmann's –
T79.6(header) - von Hippel-Lindau –
Q85.83 - von Schroetter's –
I82.890 - von Willebrand (-Jürgen) – see Disease, von Willebrand
- acquired –
D68.04– see also Disease, von Willebrand
- acquired –
- Waldenström-Kjellberg –
D50.1 - Wallenberg's –
G46.3 - wasting (syndrome) –
E88.A - water retention –
E87.79 - Waterhouse (-Friderichsen) –
A39.1 - Weber-Gubler –
G46.3 - Weber-Leyden –
G46.3 - Weber's –
G46.3 - Wegener's –
M31.30 - Weingarten's (tropical eosinophilia) –
J82.89 - Weiss-Baker –
G90.09 - Werdnig-Hoffman –
G12.0 - Wermer's –
E31.21 - Werner's –
E34.8 - Wernicke-Korsakoff (nonalcoholic) –
F04 - West's – see Epilepsy, spasms
- Westphal-Strümpell –
E83.01 - wet
- whiplash –
S13.4(header) - whistling face –
Q87.0 - Wilkie's –
K55.1 - Wilkinson-Sneddon –
L13.1 - Williams –
Q93.82 - Willebrand (-Jürgens) – see Disease, von Willebrand
- Wilson's (hepatolenticular degeneration) –
E83.01 - Wiskott-Aldrich –
D82.0 - withdrawal – see Withdrawal, state
- Woakes' (ethmoiditis) –
J33.1 - Wright's (hyperabduction) –
G54.0 - X –
I20.9 - XXXX –
Q97.1 - XXXXX –
Q97.1 - XXXXY –
Q98.1 - XXY –
Q98.0 - Yao –
M04.8 - yellow nail –
L60.5 - Zahorsky's –
B08.5 - Zellweger syndrome –
E71.510 - Zellweger-like syndrome –
E71.541
How to choose the right code
Start with the main term, then pick the indented subterm that matches the documentation (type, cause, site, laterality, episode of care). Always confirm the code in the tabular list: follow its Excludes1/Excludes2, “code first” and “use additional code” notes, and add a 7th character where required.
Source: CDC/NCHS ICD-10-CM FY2027 alphabetic index.