D82.1 – Di George's syndrome
ICD-10-CM 2027 diagnosis code · Certain disorders involving the immune mechanism
ICD-10-CM code
D82.1
- Code
D82.1(claims format:D821)- Description
- Di George's syndrome
- Billable
- Yes – valid for HIPAA-covered transactions
- Valid for
- Dates of service October 1, 2026 – September 30, 2027 (FY2027)
- Chapter
- 3. Diseases of the blood and blood-forming organs and certain disorders involving the immune mechanism (D50-D89)
- Block
- D80-D89 Certain disorders involving the immune mechanism
- Parent codes
- D82
Notes for D82.1
Applicable to:
- Pharyngeal pouch syndrome
- Thymic alymphoplasia
- Thymic aplasia or hypoplasia with immunodeficiency
Notes inherited from parent codes
Instructional notes at a category or block level apply to every code below it.
D82 – Immunodeficiency associated with other major defects
Excludes1 (not coded here):
- ataxia telangiectasia [Louis-Bar] (G11.3)
Block D80-D89
Includes:
- defects in the complement system
- immunodeficiency disorders, except human immunodeficiency virus [HIV] disease
- sarcoidosis
Excludes1 (not coded here):
Excludes2 (not included here):
- human immunodeficiency virus [HIV] disease (B20)
Index terms for D82.1
Entries in the ICD-10-CM alphabetic index that lead to this code:
- DiGeorge's syndrome
- Di George's syndrome
- Alymphoplasia, thymic
- Syndrome, di George's
- Alymphocytosis, thymic
- Pharyngeal pouch syndrome
- Syndrome, pharyngeal pouch
- Aplasia, parathyroid-thymic
- Aplasia, thymic, with immunodeficiency
- Dysplasia, thymic, with immunodeficiency
- Hypoplasia, hypoplastic, thymic, with immunodeficiency
- Hypoplasia, hypoplastic, thymus, with immunodeficiency
Related codes in D82
- D82.0 – Wiskott-Aldrich syndromeBillable
- D82.2 – Immunodeficiency with short-limbed statureBillable
- D82.3 – Immunodeficiency following hereditary defective response to Epstein-Barr virusBillable
- D82.4 – Hyperimmunoglobulin E [IgE] syndromeBillable
- D82.8 – Immunodeficiency associated with other specified major defectsBillable
- D82.9 – Immunodeficiency associated with major defect, unspecifiedBillable
Frequently asked questions
What is ICD-10 code D82.1?
D82.1 is the ICD-10-CM code for di George's syndrome, in the block D80-D89 (Certain disorders involving the immune mechanism).
Is D82.1 a billable code?
Yes. D82.1 is a billable/specific code that can be used to indicate a diagnosis for reimbursement purposes.
What category does D82.1 belong to?
It belongs to category D82 – Immunodeficiency associated with other major defects.
Source: CDC/NCHS ICD-10-CM FY2027 code files, tabular list and index. Reference only – code assignment must follow the official ICD-10-CM guidelines and documentation in the medical record.