E79.81 – Aicardi-Goutieres syndrome

ICD-10-CM 2027 diagnosis code · Metabolic disorders

Billable code

ICD-10-CM code E79.81

Code: E79.81 (claims format: E7981)
Description: Aicardi-Goutieres syndrome
Billable: Yes – valid for HIPAA-covered transactions
Valid for: Dates of service October 1, 2026 – September 30, 2027 (FY2027)
Chapter: 4. Endocrine, nutritional and metabolic diseases (E00-E89)
Block: E70-E88 Metabolic disorders
Parent codes: E79 › E79.8

Notes inherited from parent codes

Instructional notes at a category or block level apply to every code below it.

E79 – Disorders of purine and pyrimidine metabolism

Excludes1 (not coded here):

Ataxia-telangiectasia (Q87.19)
Bloom's syndrome (Q82.8)
Cockayne's syndrome (Q87.19)
calculus of kidney (N20.0)
combined immunodeficiency disorders (D81.-)
Fanconi's anemia (D61.09)
gout (M1A.-, M10.-)
orotaciduric anemia (D53.0)
progeria (E34.8)
Werner's syndrome (E34.8)
xeroderma pigmentosum (Q82.1)

Block E70-E88

Excludes1 (not coded here):

androgen insensitivity syndrome (E34.5-)
congenital adrenal hyperplasia (E25.0)
hemolytic anemias attributable to enzyme disorders (D55.-)
Marfan syndrome (Q87.4-)
5-alpha-reductase deficiency (E29.1)

Excludes2 (not included here):

Ehlers-Danlos syndromes (Q79.6-)

Index terms for E79.81

Entries in the ICD-10-CM alphabetic index that lead to this code:

Syndrome, Aicardi-Goutières

Related codes in E79.8

Frequently asked questions

What is ICD-10 code E79.81?

E79.81 is the ICD-10-CM code for aicardi-Goutieres syndrome, in the block E70-E88 (Metabolic disorders).

Is E79.81 a billable code?

Yes. E79.81 is a billable/specific code that can be used to indicate a diagnosis for reimbursement purposes.

What category does E79.81 belong to?

It belongs to category E79 – Disorders of purine and pyrimidine metabolism.

Source: CDC/NCHS ICD-10-CM FY2027 code files, tabular list and index. Reference only – code assignment must follow the official ICD-10-CM guidelines and documentation in the medical record.