E00.0 – Congenital iodine-deficiency syndrome, neurological type

ICD-10-CM 2027 diagnosis code · Disorders of thyroid gland

Billable code

ICD-10-CM code E00.0

Code: E00.0 (claims format: E000)
Description: Congenital iodine-deficiency syndrome, neurological type
Billable: Yes – valid for HIPAA-covered transactions
Valid for: Dates of service October 1, 2026 – September 30, 2027 (FY2027)
Chapter: 4. Endocrine, nutritional and metabolic diseases (E00-E89)
Block: E00-E07 Disorders of thyroid gland
Parent codes: E00

Notes for E00.0

Applicable to:

Endemic cretinism, neurological type

Notes inherited from parent codes

Instructional notes at a category or block level apply to every code below it.

E00 – Congenital iodine-deficiency syndrome

Excludes1 (not coded here):

subclinical iodine-deficiency hypothyroidism (E02)

Use additional code:

code (F70-F79) to identify associated intellectual disabilities.

Index terms for E00.0

Entries in the ICD-10-CM alphabetic index that lead to this code:

Related codes in E00

Frequently asked questions

What is ICD-10 code E00.0?

E00.0 is the ICD-10-CM code for congenital iodine-deficiency syndrome, neurological type, in the block E00-E07 (Disorders of thyroid gland).

Is E00.0 a billable code?

Yes. E00.0 is a billable/specific code that can be used to indicate a diagnosis for reimbursement purposes.

What category does E00.0 belong to?

It belongs to category E00 – Congenital iodine-deficiency syndrome.

Source: CDC/NCHS ICD-10-CM FY2027 code files, tabular list and index. Reference only – code assignment must follow the official ICD-10-CM guidelines and documentation in the medical record.