M04.8 – Other autoinflammatory syndromes
ICD-10-CM 2027 diagnosis code · Autoinflammatory syndromes (M04)
ICD-10-CM code
M04.8
- Code
M04.8(claims format:M048)- Description
- Other autoinflammatory syndromes
- Billable
- Yes – valid for HIPAA-covered transactions
- Valid for
- Dates of service October 1, 2026 – September 30, 2027 (FY2027)
- Chapter
- 13. Diseases of the musculoskeletal system and connective tissue (M00-M99)
- Block
- M04 Autoinflammatory syndromes (M04)
- Parent codes
- M04
Notes for M04.8
Applicable to:
- Blau syndrome
- Deficiency of interleukin 1 receptor antagonist [DIRA]
- Majeed syndrome
- Periodic fever, aphthous stomatitis, pharyngitis, and adenopathy syndrome [PFAPA]
- Pyogenic arthritis, pyoderma gangrenosum, and acne syndrome [PAPA]
Notes inherited from parent codes
Instructional notes at a category or block level apply to every code below it.
M04 – Autoinflammatory syndromes
Excludes2 (not included here):
- Crohn's disease (K50.-)
Index terms for M04.8
Entries in the ICD-10-CM alphabetic index that lead to this code:
- DIRA
- PAPA
- PFAPA
- Syndrome, Yao
- Syndrome, Blau
- Syndrome, Majeed
- Syndrome, autoinflammatory, specified type NEC
- Disease, diseased, autoinflammatory, NOD2-associated
- Disease, diseased, autoinflammatory, specified type NEC
- Deficiency, deficient, of interleukin 1 receptor antagonist [DIRA]
- Syndrome, pyogenic arthritis, pyoderma gangrenosum, and acne [PAPA]
- Syndrome, periodic fever, aphthous stomatitis, pharyngitis, and adenopathy [PFAPA]
Related codes in M04
Frequently asked questions
What is ICD-10 code M04.8?
M04.8 is the ICD-10-CM code for other autoinflammatory syndromes, in the block M04 (Autoinflammatory syndromes (M04)).
Is M04.8 a billable code?
Yes. M04.8 is a billable/specific code that can be used to indicate a diagnosis for reimbursement purposes.
What category does M04.8 belong to?
It belongs to category M04 – Autoinflammatory syndromes.
Source: CDC/NCHS ICD-10-CM FY2027 code files, tabular list and index. Reference only – code assignment must follow the official ICD-10-CM guidelines and documentation in the medical record.