Q87.89 – Other specified congenital malformation syndromes, not elsewhere classified
ICD-10-CM 2027 diagnosis code · Other congenital malformations
- Code
Q87.89(claims format:Q8789)- Description
- Other specified congenital malformation syndromes, not elsewhere classified
- Short description
- Oth congenital malformation syndromes, NEC
- Billable
- Yes – valid for HIPAA-covered transactions
- Valid for
- Dates of service October 1, 2026 – September 30, 2027 (FY2027)
- Chapter
- 17. Congenital malformations, deformations, chromosomal abnormalities, and genetic disorders (Q00-QA1)
- Block
- Q80-Q89 Other congenital malformations
- Parent codes
- Q87 › Q87.8
Notes inherited from parent codes
Instructional notes at a category or block level apply to every code below it.
Q87 – Other specified congenital malformation syndromes affecting multiple systems
- code(s) to identify all associated manifestations
Q87.8 – Other specified congenital malformation syndromes, not elsewhere classified
- Zellweger syndrome (E71.510)
Index terms for Q87.89
Entries in the ICD-10-CM alphabetic index that lead to this code:
- Syndrome, Glass
- Syndrome, Gorlin's
- Cantrell's syndrome
- Birt-Hogg-Dube syndrome
- Syndrome, popliteal, web
- Syndrome, Snyder-Robinson
- Syndrome, basal cell nevus
- Syndrome, Oliver-McFarlane
- Syndrome, SATB2-associated
- Cerebro-hepato-renal syndrome
- Syndrome, cardiofaciocutaneous
- Web, webbed, popliteal syndrome
- Syndrome, Birt-Hogg-Dube syndrome
- Syndrome, congenital, muscular hypertrophy-cerebral
- Syndrome, congenital, affecting multiple systems NEC
Related codes in Q87.8
- Q87.81 – Alport syndromeBillable
- Q87.82 – Arterial tortuosity syndromeBillable
- Q87.83 – Bardet-Biedl syndromeBillable
- Q87.84 – Laurence-Moon syndromeBillable
- Q87.85 – MED13L syndromeBillable
- Q87.86 – Kleefstra syndromeBillable
- Q87.87 – Hao-Fountain SyndromeBillable
- Q87.88 – CTNNB1 syndromeBillable
Frequently asked questions
What is ICD-10 code Q87.89?
Q87.89 is the ICD-10-CM code for other specified congenital malformation syndromes, not elsewhere classified, in the block Q80-Q89 (Other congenital malformations).
Is Q87.89 a billable code?
Yes. Q87.89 is a billable/specific code that can be used to indicate a diagnosis for reimbursement purposes.
What category does Q87.89 belong to?
It belongs to category Q87 – Other specified congenital malformation syndromes affecting multiple systems.
Source: CDC/NCHS ICD-10-CM FY2027 code files, tabular list and index. Reference only – code assignment must follow the official ICD-10-CM guidelines and documentation in the medical record.