E25.0 – Congenital adrenogenital disorders associated with enzyme deficiency
ICD-10-CM 2027 diagnosis code · Disorders of other endocrine glands
ICD-10-CM code
E25.0
- Code
E25.0(claims format:E250)- Description
- Congenital adrenogenital disorders associated with enzyme deficiency
- Short description
- Congenital adrenogenital disorders assoc w enzyme deficiency
- Billable
- Yes – valid for HIPAA-covered transactions
- Valid for
- Dates of service October 1, 2026 – September 30, 2027 (FY2027)
- Chapter
- 4. Endocrine, nutritional and metabolic diseases (E00-E89)
- Block
- E20-E35 Disorders of other endocrine glands
- Parent codes
- E25
Notes for E25.0
Applicable to:
- Congenital adrenal hyperplasia
- 21-Hydroxylase deficiency
- Salt-losing congenital adrenal hyperplasia
Notes inherited from parent codes
Instructional notes at a category or block level apply to every code below it.
E25 – Adrenogenital disorders
Includes:
- adrenogenital syndromes, virilizing or feminizing, whether acquired or due to adrenal hyperplasia consequent on inborn enzyme defects in hormone synthesis
- Female adrenal pseudohermaphroditism
- Female heterosexual precocious pseudopuberty
- Male isosexual precocious pseudopuberty
- Male macrogenitosomia praecox
- Male sexual precocity with adrenal hyperplasia
- Male virilization (female)
Excludes1 (not coded here):
Block E20-E35
Index terms for E25.0
Entries in the ICD-10-CM alphabetic index that lead to this code:
- Virilism, congenital
- Virilization, congenital
- Masculinization, congenital
- Adrenogenitalism, congenital
- Macrogenitosomia, congenital
- Hyperadrenocorticism, congenital
- Adrenogenital syndrome, salt loss
- Defect, defective, 21-hydroxylase
- Defect, defective, 11-hydroxylase
- Adrenogenital syndrome, congenital
- Deficiency, deficient, 11-hydroxylase
- Deficiency, deficient, 21-hydroxylase
- Pseudohermaphroditism, female, adrenal
- Hyperplasia, hyperplastic, adrenal, congenital
- Defect, defective, 3-beta-hydroxysteroid dehydrogenase
- Precocity, sexual, with adrenal hyperplasia, congenital
- Deficiency, deficient, 3-beta hydroxysteroid dehydrogenase
- Hyperplasia, hyperplastic, adrenal, congenital, salt-losing
- Hyperplasia, hyperplastic, adrenal, with, virilization, congenital
- Hyperplasia, hyperplastic, adrenal, with, sexual precocity, congenital
- Syndrome, adrenogenital, congenital, associated with enzyme deficiency
- Hyperplasia, hyperplastic, adrenal, with, virilism, adrenal, congenital
- Hyperfunction, adrenal cortex, not associated with Cushing's syndrome, virilism, congenital
Related codes in E25
Frequently asked questions
What is ICD-10 code E25.0?
E25.0 is the ICD-10-CM code for congenital adrenogenital disorders associated with enzyme deficiency, in the block E20-E35 (Disorders of other endocrine glands).
Is E25.0 a billable code?
Yes. E25.0 is a billable/specific code that can be used to indicate a diagnosis for reimbursement purposes.
What category does E25.0 belong to?
It belongs to category E25 – Adrenogenital disorders.
Source: CDC/NCHS ICD-10-CM FY2027 code files, tabular list and index. Reference only – code assignment must follow the official ICD-10-CM guidelines and documentation in the medical record.