Q99.1 – 46, XX true hermaphrodite

ICD-10-CM 2027 diagnosis code · Chromosomal abnormalities, not elsewhere classified

Billable code

ICD-10-CM code Q99.1

Code: Q99.1 (claims format: Q991)
Description: 46, XX true hermaphrodite
Billable: Yes – valid for HIPAA-covered transactions
Valid for: Dates of service October 1, 2026 – September 30, 2027 (FY2027)
Chapter: 17. Congenital malformations, deformations, chromosomal abnormalities, and genetic disorders (Q00-QA1)
Block: Q90-Q99 Chromosomal abnormalities, not elsewhere classified
Parent codes: Q99

Notes for Q99.1

Applicable to:

46, XX with streak gonads
46, XY with streak gonads
Pure gonadal dysgenesis

Notes inherited from parent codes

Instructional notes at a category or block level apply to every code below it.

Block Q90-Q99

Excludes2 (not included here):

mitochondrial metabolic disorders (E88.4-)

Index terms for Q99.1

Entries in the ICD-10-CM alphabetic index that lead to this code:

Related codes in Q99

Q99.0 – Chimera 46, XX/46, XYBillable
Q99.2 – Fragile X chromosomeBillable
Q99.8 – Other specified chromosome abnormalitiesHeader
Q99.9 – Chromosomal abnormality, unspecifiedBillable

Frequently asked questions

What is ICD-10 code Q99.1?

Q99.1 is the ICD-10-CM code for 46, XX true hermaphrodite, in the block Q90-Q99 (Chromosomal abnormalities, not elsewhere classified).

Is Q99.1 a billable code?

Yes. Q99.1 is a billable/specific code that can be used to indicate a diagnosis for reimbursement purposes.

What category does Q99.1 belong to?

It belongs to category Q99 – Other chromosome abnormalities, not elsewhere classified.

Source: CDC/NCHS ICD-10-CM FY2027 code files, tabular list and index. Reference only – code assignment must follow the official ICD-10-CM guidelines and documentation in the medical record.