D76.1 – Hemophagocytic lymphohistiocytosis
ICD-10-CM 2027 diagnosis code · Other disorders of blood and blood-forming organs
- Code
D76.1(claims format:D761)- Description
- Hemophagocytic lymphohistiocytosis
- Billable
- Yes – valid for HIPAA-covered transactions
- Valid for
- Dates of service October 1, 2026 – September 30, 2027 (FY2027)
- Chapter
- 3. Diseases of the blood and blood-forming organs and certain disorders involving the immune mechanism (D50-D89)
- Block
- D70-D77 Other disorders of blood and blood-forming organs
- Parent codes
- D76
Notes for D76.1
- Familial hemophagocytic reticulosis
- Histiocytoses of mononuclear phagocytes
Notes inherited from parent codes
Instructional notes at a category or block level apply to every code below it.
D76 – Other specified diseases with participation of lymphoreticular and reticulohistiocytic tissue
- (Abt-) Letterer-Siwe disease (C96.0)
- eosinophilic granuloma (C96.6)
- Hand-Schüller-Christian disease (C96.5)
- histiocytic medullary reticulosis (C96.9)
- histiocytic sarcoma (C96.A)
- histiocytosis X, multifocal (C96.5)
- histiocytosis X, unifocal (C96.6)
- Langerhans-cell histiocytosis, multifocal (C96.5)
- Langerhans-cell histiocytosis NOS (C96.6)
- Langerhans-cell histiocytosis, unifocal (C96.6)
- leukemic reticuloendotheliosis (C91.4-)
- lipomelanotic reticulosis (I89.8)
- malignant histiocytosis (C96.A)
- malignant reticulosis (C86.0)
- nonlipid reticuloendotheliosis (C96.0)
Index terms for D76.1
Entries in the ICD-10-CM alphabetic index that lead to this code:
Related codes in D76
Frequently asked questions
What is ICD-10 code D76.1?
D76.1 is the ICD-10-CM code for hemophagocytic lymphohistiocytosis, in the block D70-D77 (Other disorders of blood and blood-forming organs).
Is D76.1 a billable code?
Yes. D76.1 is a billable/specific code that can be used to indicate a diagnosis for reimbursement purposes.
What category does D76.1 belong to?
It belongs to category D76 – Other specified diseases with participation of lymphoreticular and reticulohistiocytic tissue.
Source: CDC/NCHS ICD-10-CM FY2027 code files, tabular list and index. Reference only – code assignment must follow the official ICD-10-CM guidelines and documentation in the medical record.