D70.0 – Congenital agranulocytosis

ICD-10-CM 2027 diagnosis code · Other disorders of blood and blood-forming organs

Billable code

ICD-10-CM code D70.0

Code: D70.0 (claims format: D700)
Description: Congenital agranulocytosis
Billable: Yes – valid for HIPAA-covered transactions
Valid for: Dates of service October 1, 2026 – September 30, 2027 (FY2027)
Chapter: 3. Diseases of the blood and blood-forming organs and certain disorders involving the immune mechanism (D50-D89)
Block: D70-D77 Other disorders of blood and blood-forming organs
Parent codes: D70

Notes for D70.0

Applicable to:

Congenital neutropenia
Infantile genetic agranulocytosis
Kostmann's disease

Notes inherited from parent codes

Instructional notes at a category or block level apply to every code below it.

D70 – Neutropenia

Includes:

agranulocytosis
decreased absolute neurophile count (ANC)

Excludes1 (not coded here):

neutropenic splenomegaly (D73.81)
transient neonatal neutropenia (P61.5)

Use additional code:

code for any associated:
fever (R50.81)

Code also:

, if applicable, mucositis (J34.81, K12.3-, K92.81, N76.81)

Index terms for D70.0

Entries in the ICD-10-CM alphabetic index that lead to this code:

Related codes in D70

D70.1 – Agranulocytosis secondary to cancer chemotherapyBillable
D70.2 – Other drug-induced agranulocytosisBillable
D70.3 – Neutropenia due to infectionBillable
D70.4 – Cyclic neutropeniaBillable
D70.8 – Other neutropeniaBillable
D70.9 – Neutropenia, unspecifiedBillable

Frequently asked questions

What is ICD-10 code D70.0?

D70.0 is the ICD-10-CM code for congenital agranulocytosis, in the block D70-D77 (Other disorders of blood and blood-forming organs).

Is D70.0 a billable code?

Yes. D70.0 is a billable/specific code that can be used to indicate a diagnosis for reimbursement purposes.

What category does D70.0 belong to?

It belongs to category D70 – Neutropenia.

Source: CDC/NCHS ICD-10-CM FY2027 code files, tabular list and index. Reference only – code assignment must follow the official ICD-10-CM guidelines and documentation in the medical record.