G11.3 – Cerebellar ataxia with defective DNA repair

ICD-10-CM 2027 diagnosis code · Systemic atrophies primarily affecting the central nervous system

Billable code

ICD-10-CM code G11.3

Code: G11.3 (claims format: G113)
Description: Cerebellar ataxia with defective DNA repair
Billable: Yes – valid for HIPAA-covered transactions
Valid for: Dates of service October 1, 2026 – September 30, 2027 (FY2027)
Chapter: 6. Diseases of the nervous system (G00-G99)
Block: G10-G14 Systemic atrophies primarily affecting the central nervous system
Parent codes: G11

Notes for G11.3

Applicable to:

Ataxia telangiectasia [Louis-Bar]

Excludes2 (not included here):

Cockayne's syndrome (Q87.19)
other disorders of purine and pyrimidine metabolism (E79.-)
xeroderma pigmentosum (Q82.1)

Notes inherited from parent codes

Instructional notes at a category or block level apply to every code below it.

G11 – Hereditary ataxia

Excludes2 (not included here):

cerebral palsy (G80.-)
hereditary and idiopathic neuropathy (G60.-)
metabolic disorders (E70-E88)

Index terms for G11.3

Entries in the ICD-10-CM alphabetic index that lead to this code:

Related codes in G11

G11.0 – Congenital nonprogressive ataxiaBillable
G11.1 – Early-onset cerebellar ataxiaHeader
G11.2 – Late-onset cerebellar ataxiaBillable
G11.4 – Hereditary spastic paraplegiaBillable
G11.5 – Hypomyelination - hypogonadotropic hypogonadism - hypodontiaBillable
G11.6 – Leukodystrophy with vanishing white matter diseaseBillable
G11.8 – Other hereditary ataxiasBillable
G11.9 – Hereditary ataxia, unspecifiedBillable

Frequently asked questions

What is ICD-10 code G11.3?

G11.3 is the ICD-10-CM code for cerebellar ataxia with defective DNA repair, in the block G10-G14 (Systemic atrophies primarily affecting the central nervous system).

Is G11.3 a billable code?

Yes. G11.3 is a billable/specific code that can be used to indicate a diagnosis for reimbursement purposes.

What category does G11.3 belong to?

It belongs to category G11 – Hereditary ataxia.

Source: CDC/NCHS ICD-10-CM FY2027 code files, tabular list and index. Reference only – code assignment must follow the official ICD-10-CM guidelines and documentation in the medical record.