M04.3 – VEXAS syndrome

ICD-10-CM 2027 diagnosis code · Autoinflammatory syndromes (M04)

Billable code New in 2027

ICD-10-CM code M04.3
Code
M04.3 (claims format: M043)
Description
VEXAS syndrome
Billable
Yes – valid for HIPAA-covered transactions
Valid for
Dates of service October 1, 2026 – September 30, 2027 (FY2027)
Chapter
13. Diseases of the musculoskeletal system and connective tissue (M00-M99)
Block
M04 Autoinflammatory syndromes (M04)
Parent codes
M04

Notes for M04.3

Applicable to:
  • Vacuoles, E1 ubiquitin-activating enzyme, X-linked, autoinflammatory, somatic syndrome
Code also:
  • any associated conditions

Notes inherited from parent codes

Instructional notes at a category or block level apply to every code below it.

M04 – Autoinflammatory syndromes

Excludes2 (not included here):
  • Crohn's disease (K50.-)

Index terms for M04.3

Entries in the ICD-10-CM alphabetic index that lead to this code:

Related codes in M04

Frequently asked questions

What is ICD-10 code M04.3?

M04.3 is the ICD-10-CM code for vEXAS syndrome, in the block M04 (Autoinflammatory syndromes (M04)).

Is M04.3 a billable code?

Yes. M04.3 is a billable/specific code that can be used to indicate a diagnosis for reimbursement purposes.

What category does M04.3 belong to?

It belongs to category M04 – Autoinflammatory syndromes.

Source: CDC/NCHS ICD-10-CM FY2027 code files, tabular list and index. Reference only – code assignment must follow the official ICD-10-CM guidelines and documentation in the medical record.