Q89.81 – Kabuki syndrome
ICD-10-CM 2027 diagnosis code · Other congenital malformations
ICD-10-CM code
Q89.81
- Code
Q89.81(claims format:Q8981)- Description
- Kabuki syndrome
- Billable
- Yes – valid for HIPAA-covered transactions
- Valid for
- Dates of service October 1, 2026 – September 30, 2027 (FY2027)
- Chapter
- 17. Congenital malformations, deformations, chromosomal abnormalities, and genetic disorders (Q00-QA1)
- Block
- Q80-Q89 Other congenital malformations
- Parent codes
- Q89 › Q89.8
Notes for Q89.81
Applicable to:
- Kabuki syndrome, type 1, due to KMT2D mutation
- Kabuki syndrome, type 2, due to KDM6A mutation
- Niikawa-Kuroki syndrome
Notes inherited from parent codes
Instructional notes at a category or block level apply to every code below it.
Q89.8 – Other specified congenital malformations
Use additional code:
- code(s) to identify all associated manifestations
Index terms for Q89.81
Entries in the ICD-10-CM alphabetic index that lead to this code:
Related codes in Q89.8
Frequently asked questions
What is ICD-10 code Q89.81?
Q89.81 is the ICD-10-CM code for kabuki syndrome, in the block Q80-Q89 (Other congenital malformations).
Is Q89.81 a billable code?
Yes. Q89.81 is a billable/specific code that can be used to indicate a diagnosis for reimbursement purposes.
What category does Q89.81 belong to?
It belongs to category Q89 – Other congenital malformations, not elsewhere classified.
Source: CDC/NCHS ICD-10-CM FY2027 code files, tabular list and index. Reference only – code assignment must follow the official ICD-10-CM guidelines and documentation in the medical record.