Q87.A – Loeys-Dietz syndrome

ICD-10-CM 2027 diagnosis code · Other congenital malformations

Billable code New in 2027

ICD-10-CM code Q87.A
Code
Q87.A (claims format: Q87A)
Description
Loeys-Dietz syndrome
Billable
Yes – valid for HIPAA-covered transactions
Valid for
Dates of service October 1, 2026 – September 30, 2027 (FY2027)
Chapter
17. Congenital malformations, deformations, chromosomal abnormalities, and genetic disorders (Q00-QA1)
Block
Q80-Q89 Other congenital malformations
Parent codes
Q87

Notes for Q87.A

Excludes1 (not coded here):
  • arterial tortuosity syndrome (Q87.82)
  • Ehlers-Danlos syndrome (Q79.6)
  • Marfan syndrome (Q87.40-Q87.43)
  • other systemic involvement of connective tissue (M35)

Notes inherited from parent codes

Instructional notes at a category or block level apply to every code below it.

Q87 – Other specified congenital malformation syndromes affecting multiple systems

Use additional code:
  • code(s) to identify all associated manifestations

Index terms for Q87.A

Entries in the ICD-10-CM alphabetic index that lead to this code:

Related codes in Q87

Frequently asked questions

What is ICD-10 code Q87.A?

Q87.A is the ICD-10-CM code for loeys-Dietz syndrome, in the block Q80-Q89 (Other congenital malformations).

Is Q87.A a billable code?

Yes. Q87.A is a billable/specific code that can be used to indicate a diagnosis for reimbursement purposes.

What category does Q87.A belong to?

It belongs to category Q87 – Other specified congenital malformation syndromes affecting multiple systems.

Source: CDC/NCHS ICD-10-CM FY2027 code files, tabular list and index. Reference only – code assignment must follow the official ICD-10-CM guidelines and documentation in the medical record.