M04.1 – Periodic fever syndromes

ICD-10-CM 2027 diagnosis code · Autoinflammatory syndromes (M04)

Billable code

ICD-10-CM code M04.1

Code: M04.1 (claims format: M041)
Description: Periodic fever syndromes
Billable: Yes – valid for HIPAA-covered transactions
Valid for: Dates of service October 1, 2026 – September 30, 2027 (FY2027)
Chapter: 13. Diseases of the musculoskeletal system and connective tissue (M00-M99)
Block: M04 Autoinflammatory syndromes (M04)
Parent codes: M04

Notes for M04.1

Applicable to:

Familial Mediterranean fever
Hyperimmunoglobin D syndrome
Mevalonate kinase deficiency
Tumor necrosis factor receptor associated periodic syndrome [TRAPS]

Notes inherited from parent codes

Instructional notes at a category or block level apply to every code below it.

M04 – Autoinflammatory syndromes

Excludes2 (not included here):

Crohn's disease (K50.-)

Index terms for M04.1

Entries in the ICD-10-CM alphabetic index that lead to this code:

Related codes in M04

M04.2 – Cryopyrin-associated periodic syndromesBillable
M04.3 – VEXAS syndromeBillable
M04.8 – Other autoinflammatory syndromesBillable
M04.9 – Autoinflammatory syndrome, unspecifiedBillable

Frequently asked questions

What is ICD-10 code M04.1?

M04.1 is the ICD-10-CM code for periodic fever syndromes, in the block M04 (Autoinflammatory syndromes (M04)).

Is M04.1 a billable code?

Yes. M04.1 is a billable/specific code that can be used to indicate a diagnosis for reimbursement purposes.

What category does M04.1 belong to?

It belongs to category M04 – Autoinflammatory syndromes.

Source: CDC/NCHS ICD-10-CM FY2027 code files, tabular list and index. Reference only – code assignment must follow the official ICD-10-CM guidelines and documentation in the medical record.