E78.3 – Hyperchylomicronemia
ICD-10-CM 2027 diagnosis code · Metabolic disorders
ICD-10-CM code
E78.3
- Code
E78.3(claims format:E783)- Description
- Hyperchylomicronemia
- Billable
- Yes – valid for HIPAA-covered transactions
- Valid for
- Dates of service October 1, 2026 – September 30, 2027 (FY2027)
- Chapter
- 4. Endocrine, nutritional and metabolic diseases (E00-E89)
- Block
- E70-E88 Metabolic disorders
- Parent codes
- E78
Notes for E78.3
Applicable to:
- Chylomicron retention disease
- Fredrickson's hyperlipoproteinemia, type I or V
- Hyperlipidemia, group D
- Mixed hyperglyceridemia
Notes inherited from parent codes
Instructional notes at a category or block level apply to every code below it.
E78 – Disorders of lipoprotein metabolism and other lipidemias
Block E70-E88
Excludes1 (not coded here):
Excludes2 (not included here):
- Ehlers-Danlos syndromes (Q79.6-)
Index terms for E78.3
Entries in the ICD-10-CM alphabetic index that lead to this code:
- Chylomicronemia
- Hyperchylomicronemia
- Syndrome, Bürger-Grütz
- Hyperglyceridemia, mixed
- Lipemia, retina, retinalis
- Lipidosis, hepatosplenomegalic
- Hepatosplenomegaly, hyperlipemic
- Disease, diseased, Bürger-Grütz
- Bürger-Grütz disease or syndrome
- Hyperlipemia, hyperlipidemia, group, D
- Disease, diseased, chylomicron retention
- Hyperlipoproteinemia, Fredrickson's type, I
- Hyperlipoproteinemia, Fredrickson's type, V
- Prebetalipoproteinemia, with chylomicronemia
- Xanthoma, with, hyperlipoproteinemia, Type I
- Xanthoma, with, hyperlipoproteinemia, Type V
- Frederickson's hyperlipoproteinemia, type, I and V
- Hyperchylomicronemia, with hyperbetalipoproteinemia
Related codes in E78
- E78.0 – Pure hypercholesterolemiaHeader
- E78.1 – Pure hyperglyceridemiaBillable
- E78.2 – Mixed hyperlipidemiaBillable
- E78.4 – Other hyperlipidemiaHeader
- E78.5 – Hyperlipidemia, unspecifiedBillable
- E78.6 – Lipoprotein deficiencyBillable
- E78.7 – Disorders of bile acid and cholesterol metabolismHeader
- E78.8 – Other disorders of lipoprotein metabolismHeader
- E78.9 – Disorder of lipoprotein metabolism, unspecifiedBillable
Frequently asked questions
What is ICD-10 code E78.3?
E78.3 is the ICD-10-CM code for hyperchylomicronemia, in the block E70-E88 (Metabolic disorders).
Is E78.3 a billable code?
Yes. E78.3 is a billable/specific code that can be used to indicate a diagnosis for reimbursement purposes.
What category does E78.3 belong to?
It belongs to category E78 – Disorders of lipoprotein metabolism and other lipidemias.
Source: CDC/NCHS ICD-10-CM FY2027 code files, tabular list and index. Reference only – code assignment must follow the official ICD-10-CM guidelines and documentation in the medical record.