D89.82 – Autoimmune lymphoproliferative syndrome [ALPS]

ICD-10-CM 2027 diagnosis code · Certain disorders involving the immune mechanism

Billable code

ICD-10-CM code D89.82

Code: D89.82 (claims format: D8982)
Description: Autoimmune lymphoproliferative syndrome [ALPS]
Billable: Yes – valid for HIPAA-covered transactions
Valid for: Dates of service October 1, 2026 – September 30, 2027 (FY2027)
Chapter: 3. Diseases of the blood and blood-forming organs and certain disorders involving the immune mechanism (D50-D89)
Block: D80-D89 Certain disorders involving the immune mechanism
Parent codes: D89 › D89.8

Notes inherited from parent codes

Instructional notes at a category or block level apply to every code below it.

D89 – Other disorders involving the immune mechanism, not elsewhere classified

Excludes1 (not coded here):

hyperglobulinemia NOS (R77.1)
monoclonal gammopathy (of undetermined significance) (D47.2)

Excludes2 (not included here):

transplant failure and rejection (T86.-)

Block D80-D89

Includes:

defects in the complement system
immunodeficiency disorders, except human immunodeficiency virus [HIV] disease
sarcoidosis

Excludes1 (not coded here):

autoimmune disease (systemic) NOS (M35.9)
functional disorders of polymorphonuclear neutrophils (D71-)

Excludes2 (not included here):

human immunodeficiency virus [HIV] disease (B20)

Index terms for D89.82

Entries in the ICD-10-CM alphabetic index that lead to this code:

Related codes in D89.8

Frequently asked questions

What is ICD-10 code D89.82?

D89.82 is the ICD-10-CM code for autoimmune lymphoproliferative syndrome [ALPS], in the block D80-D89 (Certain disorders involving the immune mechanism).

Is D89.82 a billable code?

Yes. D89.82 is a billable/specific code that can be used to indicate a diagnosis for reimbursement purposes.

What category does D89.82 belong to?

It belongs to category D89 – Other disorders involving the immune mechanism, not elsewhere classified.

Source: CDC/NCHS ICD-10-CM FY2027 code files, tabular list and index. Reference only – code assignment must follow the official ICD-10-CM guidelines and documentation in the medical record.