Q85.89 – Other phakomatoses, not elsewhere classified

ICD-10-CM 2027 diagnosis code · Other congenital malformations

Billable code

ICD-10-CM code Q85.89
Code
Q85.89 (claims format: Q8589)
Description
Other phakomatoses, not elsewhere classified
Billable
Yes – valid for HIPAA-covered transactions
Valid for
Dates of service October 1, 2026 – September 30, 2027 (FY2027)
Chapter
17. Congenital malformations, deformations, chromosomal abnormalities, and genetic disorders (Q00-QA1)
Block
Q80-Q89 Other congenital malformations
Parent codes
Q85 › Q85.8

Notes for Q85.89

Applicable to:
  • Peutz-Jeghers syndrome
  • Sturge-Weber(-Dimitri) syndrome

Notes inherited from parent codes

Instructional notes at a category or block level apply to every code below it.

Q85 – Phakomatoses, not elsewhere classified

Excludes1 (not coded here):
  • ataxia telangiectasia [Louis-Bar] (G11.3)
  • familial dysautonomia [Riley-Day] (G90.1)

Q85.8 – Other phakomatoses, not elsewhere classified

Excludes1 (not coded here):
  • Meckel-Gruber syndrome (Q61.9)

Index terms for Q85.89

Entries in the ICD-10-CM alphabetic index that lead to this code:

Related codes in Q85.8

Frequently asked questions

What is ICD-10 code Q85.89?

Q85.89 is the ICD-10-CM code for other phakomatoses, not elsewhere classified, in the block Q80-Q89 (Other congenital malformations).

Is Q85.89 a billable code?

Yes. Q85.89 is a billable/specific code that can be used to indicate a diagnosis for reimbursement purposes.

What category does Q85.89 belong to?

It belongs to category Q85 – Phakomatoses, not elsewhere classified.

Source: CDC/NCHS ICD-10-CM FY2027 code files, tabular list and index. Reference only – code assignment must follow the official ICD-10-CM guidelines and documentation in the medical record.