Q87.88 – CTNNB1 syndrome

ICD-10-CM 2027 diagnosis code · Other congenital malformations

Billable code

ICD-10-CM code Q87.88

Code: Q87.88 (claims format: Q8788)
Description: CTNNB1 syndrome
Billable: Yes – valid for HIPAA-covered transactions
Valid for: Dates of service October 1, 2026 – September 30, 2027 (FY2027)
Chapter: 17. Congenital malformations, deformations, chromosomal abnormalities, and genetic disorders (Q00-QA1)
Block: Q80-Q89 Other congenital malformations
Parent codes: Q87 › Q87.8

Notes for Q87.88

Use additional code:

code, if applicable, for associated conditions such as:
cerebral palsy (G80.-)
congenital heart malformations (Q20.0-Q24.9)
developmental disorder of speech and language (F80.-)
exudative retinopathy (H35.02-)
intellectual disability (F70-F79)
microcephaly (Q02)

Notes inherited from parent codes

Instructional notes at a category or block level apply to every code below it.

Q87 – Other specified congenital malformation syndromes affecting multiple systems

Use additional code:

code(s) to identify all associated manifestations

Q87.8 – Other specified congenital malformation syndromes, not elsewhere classified

Excludes1 (not coded here):

Zellweger syndrome (E71.510)

Index terms for Q87.88

Entries in the ICD-10-CM alphabetic index that lead to this code:

Syndrome, CTNNB1

Related codes in Q87.8

Q87.81 – Alport syndromeBillable
Q87.82 – Arterial tortuosity syndromeBillable
Q87.83 – Bardet-Biedl syndromeBillable
Q87.84 – Laurence-Moon syndromeBillable
Q87.85 – MED13L syndromeBillable
Q87.86 – Kleefstra syndromeBillable
Q87.87 – Hao-Fountain SyndromeBillable
Q87.89 – Other specified congenital malformation syndromes, not elsewhere classifiedBillable

Frequently asked questions

What is ICD-10 code Q87.88?

Q87.88 is the ICD-10-CM code for cTNNB1 syndrome, in the block Q80-Q89 (Other congenital malformations).

Is Q87.88 a billable code?

Yes. Q87.88 is a billable/specific code that can be used to indicate a diagnosis for reimbursement purposes.

What category does Q87.88 belong to?

It belongs to category Q87 – Other specified congenital malformation syndromes affecting multiple systems.

Source: CDC/NCHS ICD-10-CM FY2027 code files, tabular list and index. Reference only – code assignment must follow the official ICD-10-CM guidelines and documentation in the medical record.