ICD-10 Code for Anomaly

The default ICD-10-CM 2027 code for anomaly, anomalous (congenital) (unspecified type) is Q89.9 – Congenital malformation, unspecified. More specific codes depend on the details documented, as listed in the official index (257 codes, 250 billable).

Main code: Q89.9 – Congenital malformation, unspecified
Billable: Yes

Index entries for Anomaly

abdominal wall NEC – Q79.59
acoustic nerve – Q07.8
adrenal (gland) – Q89.1
Alder (-Reilly) (leukocyte granulation) – D72.0
alimentary tract – Q45.9
- upper – Q40.9
alveolar – M26.70
- hyperplasia – M26.79
  - mandibular – M26.72
  - maxillary – M26.71
- hypoplasia – M26.79
  - mandibular – M26.74
  - maxillary – M26.73
- ridge (process) – M26.79
- specified NEC – M26.79
ankle (joint) – Q74.2
anus – Q43.9
aorta (arch) – Q25.40
- coarctation (preductal) (postductal) – Q25.1
aortic cusp or valve – Q23.9
appendix – Q43.8
apple peel syndrome – Q41.1
aqueduct of Sylvius – Q03.0
- with spina bifida – see Spina bifida, with hydrocephalus
arm – Q74.0
arteriovenous NEC
- coronary – Q24.5
- gastrointestinal – Q27.33
  - acquired – see Angiodysplasia
artery (peripheral) – Q27.9
- basilar NEC – Q28.1
- cerebral – Q28.3
- coronary – Q24.5
- digestive system – Q27.8
- eye – Q15.8
- great – Q25.9
  - specified NEC – Q25.8
- lower limb – Q27.8
- peripheral – Q27.9
  - specified NEC – Q27.8
- pulmonary NEC – Q25.79
- renal – Q27.2
- retina – Q14.1
- specified site NEC – Q27.8
- subclavian – Q27.8
  - origin – Q25.48
- umbilical – Q27.0
- upper limb – Q27.8
- vertebral NEC – Q28.1
aryteno-epiglottic folds – Q31.8
atrial
- bands or folds – Q20.8
- septa – Q21.10
atrioventricular
- excitation – I45.6
- septum – Q21.0
auditory canal – Q17.8
auricle
- ear – Q17.8
  - causing impairment of hearing – Q16.9
- heart – Q20.8
Axenfeld's – Q15.0
back – Q89.9
band
- atrial – Q20.8
- heart – Q24.8
- ventricular – Q24.8
Bartholin's duct – Q38.4
biliary duct or passage – Q44.5
bladder – Q64.70
- absence – Q64.5
- diverticulum – Q64.6
- exstrophy – Q64.10
  - cloacal – Q64.12
  - extroversion – Q64.19
  - specified type NEC – Q64.19
  - supravesical fissure – Q64.11
- neck obstruction – Q64.31
- specified type NEC – Q64.79
bone – Q79.9
- arm – Q74.0
- face – Q75.9
- leg – Q74.2
- pelvic girdle – Q74.2
- shoulder girdle – Q74.0
- skull – Q75.9
  - with
    - anencephaly – Q00.0
    - encephalocele – see Encephalocele
    - hydrocephalus – Q03.9
      - with spina bifida – see Spina bifida, by site, with hydrocephalus
    - microcephaly – Q02
brain (multiple) – Q04.9
- vessel – Q28.3
breast – Q83.9
broad ligament – Q50.6
bronchus – Q32.4
bulbus cordis – Q21.9
bursa – Q79.9
canal of Nuck – Q52.4
canthus – Q10.3
capillary – Q27.9
cardiac – Q24.9
- chambers – Q20.9
  - specified NEC – Q20.8
- septal closure – Q21.9
  - specified NEC – Q21.8
- valve NEC – Q24.8
  - pulmonary – Q22.3
cardiovascular system – Q28.8
carpus – Q74.0
caruncle, lacrimal – Q10.6
cascade stomach – Q40.2
cauda equina – Q06.3
cecum – Q43.9
cerebral – Q04.9
- vessels – Q28.3
cervix – Q51.9
Chédiak-Higashi (-Steinbrinck) (congenital gigantism of peroxidase granules) – E70.330
cheek – Q18.9
chest wall – Q67.8
- bones – Q76.9
chin – Q18.9
chordae tendineae – Q24.8
choroid – Q14.3
- plexus – Q07.8
chromosomes, chromosomal – Q99.9
- D (1) – see condition, chromosome 13
- E (3) – see condition, chromosome 18
- G – see condition, chromosome 21
- sex
  - female phenotype – Q97.8
  - gonadal dysgenesis (pure) – Q99.1
  - Klinefelter's – Q98.4
  - male phenotype – Q98.9
  - Turner's – Q96.9
- specified NEC – Q99.8 (header)
cilia – Q10.3
circulatory system – Q28.9
clavicle – Q74.0
clitoris – Q52.6
coccyx – Q76.49
colon – Q43.9
common duct – Q44.5
communication
- coronary artery – Q24.5
- left ventricle with right atrium – Q21.0
concha (ear) – Q17.3
connection
- portal vein – Q26.5
- pulmonary venous – Q26.4
  - partial – Q26.3
  - total – Q26.2
- renal artery with kidney – Q27.2
cornea (shape) – Q13.4
coronary artery or vein – Q24.5
cranium – see Anomaly, skull
cricoid cartilage – Q31.8
cystic duct – Q44.5
dental
- alveolar – see Anomaly, alveolar
- arch relationship – M26.20
  - specified NEC – M26.29
dentofacial – M26.9
- alveolar – see Anomaly, alveolar
- dental arch relationship – M26.20
  - specified NEC – M26.29
- functional – M26.50
  - specified NEC – M26.59
- jaw-cranial base relationship – M26.10
  - asymmetry – M26.12
    - maxillary – M26.11
  - specified type NEC – M26.19
- jaw size – M26.00
  - macrogenia – M26.05
  - mandibular
    - hyperplasia – M26.03
    - hypoplasia – M26.04
  - maxillary
    - hyperplasia – M26.01
    - hypoplasia – M26.02
  - microgenia – M26.06
  - specified type NEC – M26.09
- malocclusion – M26.4
  - dental arch relationship NEC – M26.29
  - jaw-cranial base relationship – see Anomaly, dentofacial, jaw-cranial base relationship
  - jaw size – see Anomaly, dentofacial, jaw size
- specified type NEC – M26.89
- temporomandibular joint – M26.60- (header)
  - adhesions – M26.61- (header)
  - ankylosis – M26.61- (header)
  - arthralgia – M26.62- (header)
  - articular disc – M26.63- (header)
  - specified type NEC – M26.69
- tooth position, fully erupted – M26.30
  - specified NEC – M26.39
dermatoglyphic – Q82.8
diaphragm (apertures) – Q79.1
digestive organ (s) – Q45.9
- lower – Q43.9
- upper – Q40.9
distance, interarch (excessive) (inadequate) – M26.25
distribution, coronary artery – Q24.5
ductus
- arteriosus – Q25.0
- botalli – Q25.0
duodenum – Q43.9
dura (brain) – Q04.9
- spinal cord – Q06.9
ear (external) – Q17.9
- causing impairment of hearing – Q16.9
- inner – Q16.5
- middle (causing impairment of hearing) – Q16.4
- ossicles – Q16.3
Ebstein's (heart) (tricuspid valve) – Q22.5
ectodermal – Q82.9
Eisenmenger's (ventricular septal defect) – Q21.8
ejaculatory duct – Q55.4
elbow – Q74.0
endocrine gland NEC – Q89.2
epididymis – Q55.4
epiglottis – Q31.8
esophagus – Q39.9
eustachian tube – Q17.8
eye – Q15.9
- anterior segment – Q13.9
  - specified NEC – Q13.89
- posterior segment – Q14.9
  - specified NEC – Q14.8
- ptosis (eyelid) – Q10.0
- specified NEC – Q15.8
eyebrow – Q18.8
eyelid – Q10.3
- ptosis – Q10.0
face – Q18.9
- bone (s) – Q75.9
fallopian tube – Q50.6
fascia – Q79.9
femur NEC – Q74.2
fibula NEC – Q74.2
finger – Q74.0
fixation, intestine – Q43.3
flexion (joint) – Q74.9
- hip or thigh – Q65.89
foot NEC – Q74.2
- varus (congenital) – Q66.3- (header)
foramen
- Botalli – Q21.12
- ovale – Q21.12
forearm – Q74.0
forehead – Q75.8
form, teeth – K00.2
fovea centralis – Q14.1
frontal bone – see Anomaly, skull
gallbladder (position) (shape) (size) – Q44.1
Gartner's duct – Q52.4
gastrointestinal tract – Q45.9
genitalia, genital organ (s)
- female – Q52.9
  - external – Q52.70
  - internal NOS – Q52.9
- male – Q55.9
  - hydrocele – P83.5
  - specified NEC – Q55.8
genitourinary NEC
- female – Q52.9
- male – Q55.9
Gerbode – Q21.0
glottis – Q31.8
granulation or granulocyte, genetic (constitutional) (leukocyte) – D72.0
gum – Q38.6
gyri – Q07.9
hair – Q84.2
hand – Q74.0
hard tissue formation in pulp – K04.3
head – see Anomaly, skull
heart – Q24.9
- auricle – Q20.8
- bands or folds – Q24.8
- fibroelastosis cordis – I42.4
- obstructive NEC – Q22.6
- patent ductus arteriosus (Botalli) – Q25.0
- septum – Q21.9
  - auricular – Q21.19
  - interatrial – Q21.19
  - interventricular – Q21.0
    - with pulmonary stenosis or atresia, dextraposition of aorta and hypertrophy of right ventricle – Q21.3
  - specified NEC – Q21.8
  - ventricular – Q21.0
    - with pulmonary stenosis or atresia, dextraposition of aorta and hypertrophy of right ventricle – Q21.3
- tetralogy of Fallot – Q21.3
- valve NEC – Q24.8
  - aortic
    - bicuspid valve – Q23.81
      - functional, with stenosis – see Stenosis, aortic (valve)
    - insufficiency – Q23.1
    - stenosis – Q23.0
      - subaortic – Q24.4
  - mitral
    - insufficiency – Q23.3
    - stenosis – Q23.2
  - pulmonary – Q22.3
    - atresia – Q22.0
    - insufficiency – Q22.2
    - stenosis – Q22.1
      - infundibular – Q24.3
      - subvalvular – Q24.3
  - tricuspid
    - atresia – Q22.4
    - stenosis – Q22.4
- ventricle – Q20.8
heel NEC – Q74.2
Hegglin's – D72.0
hemianencephaly – Q00.0
hemicephaly – Q00.0
hemicrania – Q00.0
hepatic duct – Q44.5
hip NEC – Q74.2
hourglass stomach – Q40.2
humerus – Q74.0
hydatid of Morgagni
- female – Q50.5
- male (epididymal) – Q55.4
  - testicular – Q55.29
hymen – Q52.4
hypersegmentation of neutrophils, hereditary – D72.0
hypophyseal – Q89.2
ileocecal (coil) (valve) – Q43.9
ileum – Q43.9
ilium NEC – Q74.2
integument – Q84.9
- specified NEC – Q84.8
interarch distance (excessive) (inadequate) – M26.25
intervertebral cartilage or disc – Q76.49
intestine (large) (small) – Q43.9
- with anomalous adhesions, fixation or malrotation – Q43.3
iris – Q13.2
ischium NEC – Q74.2
jaw – see Anomaly, dentofacial
- alveolar – see Anomaly, alveolar
jaw-cranial base relationship – see Anomaly, dentofacial, jaw-cranial base relationship
jejunum – Q43.8
joint – Q74.9
- specified NEC – Q74.8
Jordan's – D72.0
kidney (s) (calyx) (pelvis) – Q63.9
- artery – Q27.2
- specified NEC – Q63.8
Klippel-Feil (brevicollis) – Q76.1
knee – Q74.1
labium (majus) (minus) – Q52.70
labyrinth, membranous – Q16.5
lacrimal apparatus or duct – Q10.6
larynx, laryngeal (muscle) – Q31.9
- web (bed) – Q31.0
lens – Q12.9
leukocytes, genetic – D72.0
- granulation (constitutional) – D72.0
lid (fold) – Q10.3
ligament – Q79.9
- broad – Q50.6
- round – Q52.8
limb – Q74.9
- lower NEC – Q74.2
  - reduction deformity – see Defect, reduction, lower limb
- upper – Q74.0
lip – Q38.0
liver – Q44.70
- duct – Q44.5
lower limb NEC – Q74.2
lumbosacral (joint) (region) – Q76.49
- kyphosis – see Kyphosis, congenital
- lordosis – see Lordosis, congenital
lung (fissure) (lobe) – Q33.9
mandible – see Anomaly, dentofacial
maxilla – see Anomaly, dentofacial
May (-Hegglin) – D72.0
meatus urinarius NEC – Q64.79
meningeal bands or folds – Q07.9
- constriction of – Q07.8
- spinal – Q06.9
meninges – Q07.9
- cerebral – Q04.8
- spinal – Q06.9
meningocele – Q05.9
mesentery – Q45.9
metacarpus – Q74.0
metatarsus NEC – Q74.2
middle ear – Q16.4
- ossicles – Q16.3
mitral (leaflets) (valve) – Q23.9
- cleft – Q23.82
- insufficiency – Q23.3
- specified NEC – Q23.88
- stenosis – Q23.2
mouth – Q38.6
Müllerian – see also Anomaly, by site
- uterus NEC – Q51.818
multiple NEC – Q89.7
muscle – Q79.9
- eyelid – Q10.3
musculoskeletal system, except limbs – Q79.9
myocardium – Q24.8
nail – Q84.6
narrowness, eyelid – Q10.3
nasal sinus (wall) – Q30.8
neck (any part) – Q18.9
nerve – Q07.9
- acoustic – Q07.8
- optic – Q07.8
nervous system (central) – Q07.9
nipple – Q83.9
nose, nasal (bones) (cartilage) (septum) (sinus) – Q30.9
- specified NEC – Q30.8
ocular muscle – Q15.8
omphalomesenteric duct – Q43.0
opening, pulmonary veins – Q26.4
optic
- disc – Q14.2
- nerve – Q07.8
opticociliary vessels – Q13.2
orbit (eye) – Q10.7
organ – Q89.9
- of Corti – Q16.5
origin
- artery
  - innominate – Q25.8
  - pulmonary – Q25.79
  - renal – Q27.2
  - subclavian – Q25.48
osseous meatus (ear) – Q16.1
ovary – Q50.39
oviduct – Q50.6
palate (hard) (soft) – Q38.5
pancreas or pancreatic duct – Q45.3
papillary muscles – Q24.8
parathyroid gland – Q89.2
paraurethral ducts – Q64.79
parotid (gland) – Q38.4
patella – Q74.1
Pelger-Huët (hereditary hyposegmentation) – D72.0
pelvic girdle NEC – Q74.2
pelvis (bony) – Q74.2
- rachitic – E64.3
penis (glans) – Q55.69
pericardium – Q24.8
peripheral vascular system – Q27.9
Peter's – Q13.4
pharynx – Q38.8
pigmentation – L81.9
- congenital – Q82.8
pituitary (gland) – Q89.2
pleural (folds) – Q34.0
portal vein – Q26.5
- connection – Q26.5
position, tooth, teeth, fully erupted – M26.30
- specified NEC – M26.39
precerebral vessel – Q28.1
prepuce – Q55.69
prostate – Q55.4
pulmonary – Q33.9
- artery NEC – Q25.79
- valve – Q22.3
  - atresia – Q22.0
  - insufficiency – Q22.2
  - specified type NEC – Q22.3
  - stenosis – Q22.1
    - infundibular – Q24.3
    - subvalvular – Q24.3
- venous connection – Q26.4
  - partial – Q26.3
  - total – Q26.2
pupil – Q13.2
- function – H57.00
  - anisocoria – H57.02
  - Argyll Robertson pupil – H57.01
  - miosis – H57.03
  - mydriasis – H57.04
  - specified type NEC – H57.09
  - tonic pupil – H57.05- (header)
pylorus – Q40.3
radius – Q74.0
rectum – Q43.9
reduction (extremity) (limb)
- femur (longitudinal) – see Defect, reduction, lower limb, longitudinal, femur
- fibula (longitudinal) – see Defect, reduction, lower limb, longitudinal, fibula
- lower limb – see Defect, reduction, lower limb
- radius (longitudinal) – see Defect, reduction, upper limb, longitudinal, radius
- tibia (longitudinal) – see Defect, reduction, lower limb, longitudinal, tibia
- ulna (longitudinal) – see Defect, reduction, upper limb, longitudinal, ulna
- upper limb – see Defect, reduction, upper limb
refraction – see Disorder, refraction
renal – Q63.9
- artery – Q27.2
- pelvis – Q63.9
  - specified NEC – Q63.8
respiratory system – Q34.9
- specified NEC – Q34.8
retina – Q14.1
rib – Q76.6
- cervical – Q76.5
Rieger – Q13.81
rotation – see Malrotation
- hip or thigh – Q65.89
round ligament – Q52.8
sacroiliac (joint) – Q74.2
sacrum NEC – Q76.49
- kyphosis – see Kyphosis, congenital
- lordosis – see Lordosis, congenital
saddle nose, syphilitic – A50.57
salivary duct or gland – Q38.4
scapula – Q74.0
scrotum – see Malformation, testis and scrotum
sebaceous gland – Q82.9
seminal vesicles – Q55.4
sense organs NEC – Q07.8
sex chromosomes NEC – see also Anomaly, chromosomes
- female phenotype – Q97.8
- male phenotype – Q98.9
shoulder (girdle) (joint) – Q74.0
sigmoid (flexure) – Q43.9
simian crease – Q82.8
sinus of Valsalva – Q25.49
skeleton generalized – Q78.9
skin (appendage) – Q82.9
skull – Q75.9
- with
  - anencephaly – Q00.0
  - encephalocele – see Encephalocele
  - hydrocephalus – Q03.9
    - with spina bifida – see Spina bifida, by site, with hydrocephalus
  - microcephaly – Q02
specified organ or site NEC – Q89.89
spermatic cord – Q55.4
spine, spinal NEC – Q76.49
- column NEC – Q76.49
  - kyphosis – see Kyphosis, congenital
  - lordosis – see Lordosis, congenital
- cord – Q06.9
- nerve root – Q07.8
spleen – Q89.09
- agenesis – Q89.01
stenonian duct – Q38.4
sternum NEC – Q76.7
stomach – Q40.3
submaxillary gland – Q38.4
tarsus NEC – Q74.2
tendon – Q79.9
testis – see Malformation, testis and scrotum
thigh NEC – Q74.2
thorax (wall) – Q67.8
- bony – Q76.9
throat – Q38.8
thumb – Q74.0
thymus gland – Q89.2
thyroid (gland) – Q89.2
- cartilage – Q31.8
tibia NEC – Q74.2
- saber – A50.56
toe – Q74.2
tongue – Q38.3
tooth, teeth – K00.9
- eruption – K00.6
- position, fully erupted – M26.30
- spacing, fully erupted – M26.30
trachea (cartilage) – Q32.1
tragus – Q17.9
tricuspid (leaflet) (valve) – Q22.9
- atresia or stenosis – Q22.4
- Ebstein's – Q22.5
Uhl's (hypoplasia of myocardium, right ventricle) – Q24.8
ulna – Q74.0
umbilical artery – Q27.0
union
- cricoid cartilage and thyroid cartilage – Q31.8
- thyroid cartilage and hyoid bone – Q31.8
- trachea with larynx – Q31.8
upper limb – Q74.0
urachus – Q64.4
ureter – Q62.8
- obstructive NEC – Q62.39
  - cecoureterocele – Q62.32
  - orthotopic ureterocele – Q62.31
urethra – Q64.70
- absence – Q64.5
- double – Q64.74
- fistula to rectum – Q64.73
- obstructive – Q64.39
  - stricture – Q64.32
- prolapse – Q64.71
- specified type NEC – Q64.79
urinary tract – Q64.9
uterus – Q51.9
- with only one functioning horn – Q51.4
uvula – Q38.5
vagina – Q52.4
valleculae – Q31.8
valve (heart) – Q24.8
- coronary sinus – Q24.5
- inferior vena cava – Q24.8
- pulmonary – Q22.3
- sinus coronario – Q24.5
- venae cavae inferioris – Q24.8
vas deferens – Q55.4
vascular – Q27.9
- brain – Q28.3
- ring – Q25.45
vein (s) (peripheral) – Q27.9
- brain – Q28.3
- cerebral – Q28.3
- coronary – Q24.5
- developmental – Q28.3
- great – Q26.9
  - specified NEC – Q26.8
vena cava (inferior) (superior) – Q26.9
venous – see Anomaly, vein(s)
venous return – Q26.8
ventricular
- bands or folds – Q24.8
- septa – Q21.0
vertebra – Q76.49
- kyphosis – see Kyphosis, congenital
- lordosis – see Lordosis, congenital
vesicourethral orifice – Q64.79
vessel (s) – Q27.9
- optic papilla – Q14.2
- precerebral – Q28.1
vitelline duct – Q43.0
vitreous body or humor – Q14.0
vulva – Q52.70
wrist (joint) – Q74.0

How to choose the right code

Start with the main term, then pick the indented subterm that matches the documentation (type, cause, site, laterality, episode of care). Always confirm the code in the tabular list: follow its Excludes1/Excludes2, “code first” and “use additional code” notes, and add a 7th character where required.

Source: CDC/NCHS ICD-10-CM FY2027 alphabetic index.