Q00.0 – Anencephaly
ICD-10-CM 2027 diagnosis code · Congenital malformations of the nervous system
ICD-10-CM code
Q00.0
- Code
Q00.0(claims format:Q000)- Description
- Anencephaly
- Billable
- Yes – valid for HIPAA-covered transactions
- Valid for
- Dates of service October 1, 2026 – September 30, 2027 (FY2027)
- Chapter
- 17. Congenital malformations, deformations, chromosomal abnormalities, and genetic disorders (Q00-QA1)
- Block
- Q00-Q07 Congenital malformations of the nervous system
- Parent codes
- Q00
Notes for Q00.0
Applicable to:
- Acephaly
- Acrania
- Amyelencephaly
- Hemianencephaly
- Hemicephaly
Index terms for Q00.0
Entries in the ICD-10-CM alphabetic index that lead to this code:
- Acrania
- Absence, brain
- Aplasia, brain
- Agenesis, brain
- Hemianencephaly
- Hemicephalus, hemicephaly
- Anencephalus, anencephaly
- Anomaly, anomalous, hemicrania
- Monster, monstrosity, acephalic
- Anomaly, anomalous, hemicephaly
- Amyelencephalus, amyelencephaly
- Agenesis, skull, with, anencephaly
- Anomaly, anomalous, hemianencephaly
- Hemicrania, congenital malformation
- Absence, skull bone, with, anencephaly
- Distortion, skull bone, with, anencephalus
- Acephalia, acephalism, acephalus, acephaly
- Anomaly, anomalous, skull, with, anencephaly
- Imperfect, closure, skull, with, anencephaly
- Deformity, skull, congenital, with, anencephaly
- Hypoplasia, hypoplastic, skull, with, anencephaly
- Anomaly, anomalous, bone, skull, with, anencephaly
Related codes in Q00
- Q00.1 – CraniorachischisisBillable
- Q00.2 – IniencephalyBillable
Frequently asked questions
What is ICD-10 code Q00.0?
Q00.0 is the ICD-10-CM code for anencephaly, in the block Q00-Q07 (Congenital malformations of the nervous system).
Is Q00.0 a billable code?
Yes. Q00.0 is a billable/specific code that can be used to indicate a diagnosis for reimbursement purposes.
What category does Q00.0 belong to?
It belongs to category Q00 – Anencephaly and similar malformations.
Source: CDC/NCHS ICD-10-CM FY2027 code files, tabular list and index. Reference only – code assignment must follow the official ICD-10-CM guidelines and documentation in the medical record.