ICD-10 Code for Defect

The default ICD-10-CM 2027 code for defect, defective is Q89.9 – Congenital malformation, unspecified. More specific codes depend on the details documented, as listed in the official index (121 codes, 96 billable).

Main code: Q89.9 – Congenital malformation, unspecified
Billable: Yes

Index entries for Defect

3-beta-hydroxysteroid dehydrogenase – E25.0
11-hydroxylase – E25.0
21-hydroxylase – E25.0
abdominal wall, congenital – Q79.59
antibody immunodeficiency – D80.9
aorticopulmonary septum – Q21.4
atrial septal – Q21.10
- coronary sinus – Q21.13
- following acute myocardial infarction (current complication) – I23.1
- ostium primum type (type I) – Q21.20
  - with
    - common atrioventricular valves and moderate or larger inlet VSD – Q21.23
    - separate atrioventricular valves – Q21.21
      - and small or restrictive inlet VSD – Q21.22
- ostium secundum type (patent persistent) (type II) – Q21.11
- sinus venosus – Q21.16
  - inferior – Q21.15
  - superior – Q21.14
- specified NEC – Q21.19
- vena cava type
  - inferior – Q21.15
  - superior – Q21.14
atrioventricular
- canal – Q21.20
- septal
  - common – Q21.23
  - complete – Q21.23
  - incomplete – Q21.21
  - intermediate – Q21.22
  - partial – Q21.21
  - transitional – Q21.22
  - unspecified as to partial or complete – Q21.20
- septum – Q21.20
auricular septal – Q21.10
bilirubin excretion NEC – E80.6
biosynthesis, androgen (testicular) – E29.1
bulbar septum – Q21.0
catalase – E80.3
cell membrane receptor complex (CR3) – D71.8
circulation – I99.9
- congenital – Q28.9
- newborn – Q28.9
coagulation (factor) – D68.9 – see also Deficiency, factor
- with
  - COVID-19 associated coagulopathy – D68.8
  - ectopic pregnancy – O08.1
  - molar pregnancy – O08.1
- acquired – D68.4
- antepartum with hemorrhage – see Hemorrhage, antepartum, with coagulation defect
- due to
  - liver disease – D68.4
  - vitamin K deficiency – D68.4
- hereditary NEC – D68.2
- intrapartum – O67.0
- newborn, transient – P61.6
- postpartum – O99.13
  - with hemorrhage – O72.3
- specified type NEC – D68.8
complement system – D84.1
conduction (heart) – I45.9
- bone – see Deafness, conductive
congenital, organ or site not listed – see Anomaly, by site
coronary sinus – Q21.13
cushion, endocardial – Q21.20
- common – Q21.23
- incomplete – Q21.21
- intermediate – Q21.22
- transitional – Q21.22
degradation, glycoprotein – E77.1
dental bridge, crown, fillings – see Defect, dental restoration
dental restoration – K08.50
- specified NEC – K08.59
dentin (hereditary) – K00.5
Descemet's membrane, congenital – Q13.89
developmental – see also Anomaly
- cauda equina – Q06.3
diaphragm
- with elevation, eventration or hernia – see Hernia, diaphragm
- congenital – Q79.1
  - with hernia – Q79.0
  - gross (with hernia) – Q79.0
ectodermal, congenital – Q82.9
Eisenmenger's – Q21.8
enzyme
- catalase – E80.3
- peroxidase – E80.3
esophagus, congenital – Q39.9
extensor retinaculum – M62.89
fibrin polymerization – D68.2
filling
- bladder – R93.41
- kidney – R93.42- (header)
- renal pelvis – R93.41
- stomach – R93.3
- ureter – R93.41
- urinary organs, specified NEC – R93.49
GABA (gamma aminobutyric acid) – E72.81
Gerbode – Q21.0
glucose transport, blood-brain barrier – E74.810
glycoprotein degradation – E77.1
Hageman (factor) – D68.2
hearing – see Deafness
high grade – F70
home, technical, preventing adequate care – Z59.19
interatrial septal – Q21.19
interauricular septal – Q21.19
interventricular septal – Q21.0
- with dextroposition of aorta, pulmonary stenosis and hypertrophy of right ventricle – Q21.3
- in tetralogy of Fallot – Q21.3
intervertebral annular fibrosis – M51.9 – see also Disease, intervertebral disc, by site
- lumbar – M51.A0
  - large – M51.A2
  - small – M51.A1
- lumbosacral – M51.A3
  - large – M51.A5
  - small – M51.A4
learning (specific) – see Disorder, learning
lymphocyte function antigen-1 (LFA-1) – D84.0
lysosomal enzyme, post-translational modification – E77.0
major osseous – M89.70
- ankle – M89.77- (header)
- carpus – M89.74- (header)
- clavicle – M89.71- (header)
- femur – M89.75- (header)
- fibula – M89.76- (header)
- fingers – M89.74- (header)
- foot – M89.77- (header)
- forearm – M89.73- (header)
- hand – M89.74- (header)
- humerus – M89.72- (header)
- lower leg – M89.76- (header)
- metacarpus – M89.74- (header)
- metatarsus – M89.77- (header)
- multiple sites – M89.79
- pelvic region – M89.75- (header)
- pelvis – M89.75- (header)
- radius – M89.73- (header)
- scapula – M89.71- (header)
- shoulder region – M89.71- (header)
- specified NEC – M89.78
- tarsus – M89.77- (header)
- thigh – M89.75- (header)
- tibia – M89.76- (header)
- toes – M89.77- (header)
- ulna – M89.73- (header)
mental – see Disability, intellectual
modification, lysosomal enzymes, post-translational – E77.0
obstructive, congenital
- renal pelvis – Q62.39
- ureter – Q62.39
  - atresia – see Atresia, ureter
  - cecoureterocele – Q62.32
  - megaureter – Q62.2
  - orthotopic ureterocele – Q62.31
osseous, major – M89.70
- ankle – M89.77- (header)
- carpus – M89.74- (header)
- clavicle – M89.71- (header)
- femur – M89.75- (header)
- fibula – M89.76- (header)
- fingers – M89.74- (header)
- foot – M89.77- (header)
- forearm – M89.73- (header)
- hand – M89.74- (header)
- humerus – M89.72- (header)
- lower leg – M89.76- (header)
- metacarpus – M89.74- (header)
- metatarsus – M89.77- (header)
- multiple sites – M89.9
- pelvic region – M89.75- (header)
- pelvis – M89.75- (header)
- radius – M89.73- (header)
- scapula – M89.71- (header)
- shoulder region – M89.71- (header)
- specified NEC – M89.78
- tarsus – M89.77- (header)
- thigh – M89.75- (header)
- tibia – M89.76- (header)
- toes – M89.77- (header)
- ulna – M89.73- (header)
osteochondral NEC – M95.8 – see also Deformity
ostium
- primum – Q21.20
- secundum – Q21.11
peroxidase – E80.3
placental blood supply – see Insufficiency, placental
platelets, qualitative – D69.19
- constitutional – see Disease, von Willebrand
postural NEC, spine – see Dorsopathy, deforming
qualitative, of von Willebrand factor
- with
  - decreased platelet adhesion and selective deficiency of high-molecular-weight multimers – D68.020 – see also Disease, von Willebrand
  - defective platelet adhesion with a normal size distribution of von Willebrand factor multimers – D68.022 – see also Disease, von Willebrand
  - defective von Willebrand factor to factor VIII binding – D68.023 – see also Disease, von Willebrand
  - high-molecular-weight von Willebrand factor loss – D68.021 – see also Disease, von Willebrand
  - hyper-adhesive forms – D68.021 – see also Disease, von Willebrand
  - increased affinity for platelet glycoprotein lb – D68.021 – see also Disease, von Willebrand
  - markedly decreased affinity for factor VIII – D68.023 – see also Disease, von Willebrand
- in von Willebrand factor function, with no further subtyping – D68.029 – see also Disease, von Willebrand
reduction
- limb – Q73.8
  - lower – Q72.9- (header)
    - absence – see Agenesis, leg
      - foot – see Agenesis, foot
    - longitudinal
      - femur – Q72.4- (header)
      - fibula – Q72.6- (header)
      - tibia – Q72.5- (header)
    - specified type NEC – Q72.89- (header)
    - split foot – Q72.7- (header)
  - specified type NEC – Q73.8
  - upper – Q71.9- (header)
    - absence – see Agenesis, arm
      - forearm – see Agenesis, forearm
      - hand – see Agenesis, hand
    - lobster-claw hand – Q71.6- (header)
    - longitudinal
      - radius – Q71.4- (header)
      - ulna – Q71.5- (header)
    - specified type NEC – Q71.89- (header)
renal pelvis – Q63.8
- obstructive – Q62.39
respiratory system, congenital – Q34.9
restoration, dental – K08.50
- specified NEC – K08.59
retinal nerve bundle fibers – H35.89
septal (heart) – Q21.9
- acquired (atrial) (auricular) (ventricular) (old) – I51.0
- atrial – Q21.10 – see also Defect, atrial septal
  - concurrent with acute myocardial infarction – see Infarct, myocardium
  - following acute myocardial infarction (current complication) – I23.1
- ventricular – Q21.0 – see also Defect, ventricular septal
sinus venosus – Q21.16 – see also Defect, atrial septal, sinus venosus
speech – see Disorder, speech
- developmental – F80.9
- specified NEC – R47.89
Taussig-Bing (aortic transposition and overriding pulmonary artery) – Q20.1
teeth, wedge – K03.1
vascular (local) – I99.9
- congenital – Q27.9
ventricular septal – Q21.0
- concurrent with acute myocardial infarction – see Infarct, myocardium
- following acute myocardial infarction (current complication) – I23.2
- in tetralogy of Fallot – Q21.3
vision NEC – H54.7
visual field – H53.40
- bilateral
  - heteronymous – H53.47
  - homonymous – H53.46- (header)
- generalized contraction – H53.48- (header)
- localized
  - arcuate – H53.43- (header)
  - scotoma (central area) – H53.41- (header)
    - blind spot area – H53.42- (header)
  - sector – H53.43- (header)
  - specified type NEC – H53.45- (header)
voice – R49.9
- specified NEC – R49.8
wedge, tooth, teeth (abrasion) – K03.1

How to choose the right code

Start with the main term, then pick the indented subterm that matches the documentation (type, cause, site, laterality, episode of care). Always confirm the code in the tabular list: follow its Excludes1/Excludes2, “code first” and “use additional code” notes, and add a 7th character where required.

Source: CDC/NCHS ICD-10-CM FY2027 alphabetic index.