Q03.0 – Malformations of aqueduct of Sylvius

ICD-10-CM 2027 diagnosis code · Congenital malformations of the nervous system

Billable code

ICD-10-CM code Q03.0

Code: Q03.0 (claims format: Q030)
Description: Malformations of aqueduct of Sylvius
Billable: Yes – valid for HIPAA-covered transactions
Valid for: Dates of service October 1, 2026 – September 30, 2027 (FY2027)
Chapter: 17. Congenital malformations, deformations, chromosomal abnormalities, and genetic disorders (Q00-QA1)
Block: Q00-Q07 Congenital malformations of the nervous system
Parent codes: Q03

Notes for Q03.0

Applicable to:

Anomaly of aqueduct of Sylvius
Obstruction of aqueduct of Sylvius, congenital
Stenosis of aqueduct of Sylvius

Notes inherited from parent codes

Instructional notes at a category or block level apply to every code below it.

Q03 – Congenital hydrocephalus

Includes:

hydrocephalus in newborn

Excludes1 (not coded here):

Arnold-Chiari syndrome, type II (Q07.0-)
acquired hydrocephalus (G91.-)
hydrocephalus due to congenital toxoplasmosis (P37.1)
hydrocephalus with spina bifida (Q05.0-Q05.4)

Index terms for Q03.0

Entries in the ICD-10-CM alphabetic index that lead to this code:

Related codes in Q03

Q03.1 – Atresia of foramina of Magendie and LuschkaBillable
Q03.8 – Other congenital hydrocephalusBillable
Q03.9 – Congenital hydrocephalus, unspecifiedBillable

Frequently asked questions

What is ICD-10 code Q03.0?

Q03.0 is the ICD-10-CM code for malformations of aqueduct of Sylvius, in the block Q00-Q07 (Congenital malformations of the nervous system).

Is Q03.0 a billable code?

Yes. Q03.0 is a billable/specific code that can be used to indicate a diagnosis for reimbursement purposes.

What category does Q03.0 belong to?

It belongs to category Q03 – Congenital hydrocephalus.

Source: CDC/NCHS ICD-10-CM FY2027 code files, tabular list and index. Reference only – code assignment must follow the official ICD-10-CM guidelines and documentation in the medical record.