E74.01 – von Gierke disease
ICD-10-CM 2027 diagnosis code · Metabolic disorders
ICD-10-CM code
E74.01
- Code
E74.01(claims format:E7401)- Description
- von Gierke disease
- Billable
- Yes – valid for HIPAA-covered transactions
- Valid for
- Dates of service October 1, 2026 – September 30, 2027 (FY2027)
- Chapter
- 4. Endocrine, nutritional and metabolic diseases (E00-E89)
- Block
- E70-E88 Metabolic disorders
- Parent codes
- E74 › E74.0
Notes for E74.01
Applicable to:
- Type I glycogen storage disease
Notes inherited from parent codes
Instructional notes at a category or block level apply to every code below it.
E74 – Other disorders of carbohydrate metabolism
Excludes1 (not coded here):
Block E70-E88
Excludes1 (not coded here):
Excludes2 (not included here):
- Ehlers-Danlos syndromes (Q79.6-)
Index terms for E74.01
Entries in the ICD-10-CM alphabetic index that lead to this code:
- Gierke's disease
- Von Gierke's disease
- Disease, diseased, Gierke's
- Van Creveld-von Gierke disease
- Disease, diseased, von Gierke's
- Disease, diseased, van Creveld-von Gierke
- Disease, diseased, glycogen storage, type I
- Deficiency, deficient, glucose-6-phosphatase
- Disease, diseased, glycogen storage, Von Gierke's
- Disease, diseased, glycogen storage, glucose-6-phosphatase deficiency
Related codes in E74.0
Frequently asked questions
What is ICD-10 code E74.01?
E74.01 is the ICD-10-CM code for von Gierke disease, in the block E70-E88 (Metabolic disorders).
Is E74.01 a billable code?
Yes. E74.01 is a billable/specific code that can be used to indicate a diagnosis for reimbursement purposes.
What category does E74.01 belong to?
It belongs to category E74 – Other disorders of carbohydrate metabolism.
Source: CDC/NCHS ICD-10-CM FY2027 code files, tabular list and index. Reference only – code assignment must follow the official ICD-10-CM guidelines and documentation in the medical record.