E74.0 – Glycogen storage disease
ICD-10-CM 2027 diagnosis code · Metabolic disorders
ICD-10-CM code
E74.0
- Code
E74.0(claims format:E740)- Description
- Glycogen storage disease
- Billable
- No – use a more specific code below
- Valid for
- Dates of service October 1, 2026 – September 30, 2027 (FY2027)
- Chapter
- 4. Endocrine, nutritional and metabolic diseases (E00-E89)
- Block
- E70-E88 Metabolic disorders
- Parent codes
- E74
Billable codes under E74.0
E74.0 is a header code and cannot be used on claims. Choose the most specific code:
- E74.00 – Glycogen storage disease, unspecifiedBillable
- E74.01 – von Gierke diseaseBillable
- E74.02 – Pompe diseaseBillable
- E74.03 – Cori diseaseBillable
- E74.04 – McArdle diseaseBillable
- E74.05 – Lysosome-associated membrane protein 2 [LAMP2] deficiencyBillable
- E74.09 – Other glycogen storage diseaseBillable
Notes inherited from parent codes
Instructional notes at a category or block level apply to every code below it.
E74 – Other disorders of carbohydrate metabolism
Excludes1 (not coded here):
Block E70-E88
Excludes1 (not coded here):
Excludes2 (not included here):
- Ehlers-Danlos syndromes (Q79.6-)
Related codes in E74
- E74.1 – Disorders of fructose metabolismHeader
- E74.2 – Disorders of galactose metabolismHeader
- E74.3 – Other disorders of intestinal carbohydrate absorptionHeader
- E74.4 – Disorders of pyruvate metabolism and gluconeogenesisBillable
- E74.8 – Other specified disorders of carbohydrate metabolismHeader
- E74.9 – Disorder of carbohydrate metabolism, unspecifiedBillable
Frequently asked questions
What is ICD-10 code E74.0?
E74.0 is the ICD-10-CM code for glycogen storage disease, in the block E70-E88 (Metabolic disorders).
Is E74.0 a billable code?
No. E74.0 is a header code with more specific child codes; report one of the billable codes listed above.
What category does E74.0 belong to?
It belongs to category E74 – Other disorders of carbohydrate metabolism.
Source: CDC/NCHS ICD-10-CM FY2027 code files, tabular list and index. Reference only – code assignment must follow the official ICD-10-CM guidelines and documentation in the medical record.