Q87.4 – Marfan syndrome
ICD-10-CM 2027 diagnosis code · Other congenital malformations
ICD-10-CM code
Q87.4
- Code
Q87.4(claims format:Q874)- Description
- Marfan syndrome
- Billable
- No – use a more specific code below
- Valid for
- Dates of service October 1, 2026 – September 30, 2027 (FY2027)
- Chapter
- 17. Congenital malformations, deformations, chromosomal abnormalities, and genetic disorders (Q00-QA1)
- Block
- Q80-Q89 Other congenital malformations
- Parent codes
- Q87
Billable codes under Q87.4
Q87.4 is a header code and cannot be used on claims. Choose the most specific code:
- Q87.40 – Marfan syndrome, unspecifiedBillable
- Q87.41 – Marfan syndrome with cardiovascular manifestationsHeader (more codes below)
- Q87.42 – Marfan syndrome with ocular manifestationsBillable
- Q87.43 – Marfan syndrome with skeletal manifestationBillable
Notes inherited from parent codes
Instructional notes at a category or block level apply to every code below it.
Q87 – Other specified congenital malformation syndromes affecting multiple systems
Use additional code:
- code(s) to identify all associated manifestations
Related codes in Q87
- Q87.0 – Congenital malformation syndromes predominantly affecting facial appearanceBillable
- Q87.1 – Congenital malformation syndromes predominantly associated with short statureHeader
- Q87.2 – Congenital malformation syndromes predominantly involving limbsBillable
- Q87.3 – Congenital malformation syndromes involving early overgrowthBillable
- Q87.5 – Other congenital malformation syndromes with other skeletal changesBillable
- Q87.8 – Other specified congenital malformation syndromes, not elsewhere classifiedHeader
- Q87.A – Loeys-Dietz syndromeBillable
Frequently asked questions
What is ICD-10 code Q87.4?
Q87.4 is the ICD-10-CM code for marfan syndrome, in the block Q80-Q89 (Other congenital malformations).
Is Q87.4 a billable code?
No. Q87.4 is a header code with more specific child codes; report one of the billable codes listed above.
What category does Q87.4 belong to?
It belongs to category Q87 – Other specified congenital malformation syndromes affecting multiple systems.
Source: CDC/NCHS ICD-10-CM FY2027 code files, tabular list and index. Reference only – code assignment must follow the official ICD-10-CM guidelines and documentation in the medical record.