Q85.8 – Other phakomatoses, not elsewhere classified

ICD-10-CM 2027 diagnosis code · Other congenital malformations

Non-billable header

ICD-10-CM code Q85.8

Code: Q85.8 (claims format: Q858)
Description: Other phakomatoses, not elsewhere classified
Billable: No – use a more specific code below
Valid for: Dates of service October 1, 2026 – September 30, 2027 (FY2027)
Chapter: 17. Congenital malformations, deformations, chromosomal abnormalities, and genetic disorders (Q00-QA1)
Block: Q80-Q89 Other congenital malformations
Parent codes: Q85

Billable codes under Q85.8

Q85.8 is a header code and cannot be used on claims. Choose the most specific code:

Q85.81 – PTEN hamartoma tumor syndromeBillable
Q85.82 – Other Cowden syndromeBillable
Q85.83 – Von Hippel-Lindau syndromeBillable
Q85.89 – Other phakomatoses, not elsewhere classifiedBillable

Notes for Q85.8

Excludes1 (not coded here):

Meckel-Gruber syndrome (Q61.9)

Notes inherited from parent codes

Instructional notes at a category or block level apply to every code below it.

Q85 – Phakomatoses, not elsewhere classified

Excludes1 (not coded here):

ataxia telangiectasia [Louis-Bar] (G11.3)
familial dysautonomia [Riley-Day] (G90.1)

Related codes in Q85

Q85.0 – Neurofibromatosis (nonmalignant)Header
Q85.1 – Tuberous sclerosisBillable
Q85.9 – Phakomatosis, unspecifiedBillable

Frequently asked questions

What is ICD-10 code Q85.8?

Q85.8 is the ICD-10-CM code for other phakomatoses, not elsewhere classified, in the block Q80-Q89 (Other congenital malformations).

Is Q85.8 a billable code?

No. Q85.8 is a header code with more specific child codes; report one of the billable codes listed above.

What category does Q85.8 belong to?

It belongs to category Q85 – Phakomatoses, not elsewhere classified.

Source: CDC/NCHS ICD-10-CM FY2027 code files, tabular list and index. Reference only – code assignment must follow the official ICD-10-CM guidelines and documentation in the medical record.