G11 – Hereditary ataxia
ICD-10-CM 2027 diagnosis code · Systemic atrophies primarily affecting the central nervous system
ICD-10-CM code
G11
- Code
G11(claims format:G11)- Description
- Hereditary ataxia
- Billable
- No – use a more specific code below
- Valid for
- Dates of service October 1, 2026 – September 30, 2027 (FY2027)
- Chapter
- 6. Diseases of the nervous system (G00-G99)
- Block
- G10-G14 Systemic atrophies primarily affecting the central nervous system
Billable codes under G11
G11 is a header code and cannot be used on claims. Choose the most specific code:
- G11.0 – Congenital nonprogressive ataxiaBillable
- G11.1 – Early-onset cerebellar ataxiaHeader (more codes below)
- G11.2 – Late-onset cerebellar ataxiaBillable
- G11.3 – Cerebellar ataxia with defective DNA repairBillable
- G11.4 – Hereditary spastic paraplegiaBillable
- G11.5 – Hypomyelination - hypogonadotropic hypogonadism - hypodontiaBillable
- G11.6 – Leukodystrophy with vanishing white matter diseaseBillable
- G11.8 – Other hereditary ataxiasBillable
- G11.9 – Hereditary ataxia, unspecifiedBillable
Notes for G11
Frequently asked questions
What is ICD-10 code G11?
G11 is the ICD-10-CM code for hereditary ataxia, in the block G10-G14 (Systemic atrophies primarily affecting the central nervous system).
Is G11 a billable code?
No. G11 is a header code with more specific child codes; report one of the billable codes listed above.
Source: CDC/NCHS ICD-10-CM FY2027 code files, tabular list and index. Reference only – code assignment must follow the official ICD-10-CM guidelines and documentation in the medical record.