E84.1 – Cystic fibrosis with intestinal manifestations

ICD-10-CM 2027 diagnosis code · Metabolic disorders

Non-billable header

ICD-10-CM code E84.1

Code: E84.1 (claims format: E841)
Description: Cystic fibrosis with intestinal manifestations
Billable: No – use a more specific code below
Valid for: Dates of service October 1, 2026 – September 30, 2027 (FY2027)
Chapter: 4. Endocrine, nutritional and metabolic diseases (E00-E89)
Block: E70-E88 Metabolic disorders
Parent codes: E84

Billable codes under E84.1

E84.1 is a header code and cannot be used on claims. Choose the most specific code:

Notes inherited from parent codes

Instructional notes at a category or block level apply to every code below it.

E84 – Cystic fibrosis

Includes:

mucoviscidosis

Code also:

exocrine pancreatic insufficiency (K86.81)

Block E70-E88

Excludes1 (not coded here):

androgen insensitivity syndrome (E34.5-)
congenital adrenal hyperplasia (E25.0)
hemolytic anemias attributable to enzyme disorders (D55.-)
Marfan syndrome (Q87.4-)
5-alpha-reductase deficiency (E29.1)

Excludes2 (not included here):

Ehlers-Danlos syndromes (Q79.6-)

Related codes in E84

E84.0 – Cystic fibrosis with pulmonary manifestationsBillable
E84.8 – Cystic fibrosis with other manifestationsBillable
E84.9 – Cystic fibrosis, unspecifiedBillable

Frequently asked questions

What is ICD-10 code E84.1?

E84.1 is the ICD-10-CM code for cystic fibrosis with intestinal manifestations, in the block E70-E88 (Metabolic disorders).

Is E84.1 a billable code?

No. E84.1 is a header code with more specific child codes; report one of the billable codes listed above.

What category does E84.1 belong to?

It belongs to category E84 – Cystic fibrosis.

Source: CDC/NCHS ICD-10-CM FY2027 code files, tabular list and index. Reference only – code assignment must follow the official ICD-10-CM guidelines and documentation in the medical record.