E84.0 – Cystic fibrosis with pulmonary manifestations

ICD-10-CM 2027 diagnosis code · Metabolic disorders

Billable code

ICD-10-CM code E84.0

Code: E84.0 (claims format: E840)
Description: Cystic fibrosis with pulmonary manifestations
Billable: Yes – valid for HIPAA-covered transactions
Valid for: Dates of service October 1, 2026 – September 30, 2027 (FY2027)
Chapter: 4. Endocrine, nutritional and metabolic diseases (E00-E89)
Block: E70-E88 Metabolic disorders
Parent codes: E84

Notes for E84.0

Use additional code:

code to identify any infectious organism present, such as:
Pseudomonas (B96.5)

Notes inherited from parent codes

Instructional notes at a category or block level apply to every code below it.

E84 – Cystic fibrosis

Includes:

mucoviscidosis

Code also:

exocrine pancreatic insufficiency (K86.81)

Block E70-E88

Excludes1 (not coded here):

androgen insensitivity syndrome (E34.5-)
congenital adrenal hyperplasia (E25.0)
hemolytic anemias attributable to enzyme disorders (D55.-)
Marfan syndrome (Q87.4-)
5-alpha-reductase deficiency (E29.1)

Excludes2 (not included here):

Ehlers-Danlos syndromes (Q79.6-)

Index terms for E84.0

Entries in the ICD-10-CM alphabetic index that lead to this code:

Fibrosis, fibrotic, cystic, with, pulmonary manifestations

Related codes in E84

Frequently asked questions

What is ICD-10 code E84.0?

E84.0 is the ICD-10-CM code for cystic fibrosis with pulmonary manifestations, in the block E70-E88 (Metabolic disorders).

Is E84.0 a billable code?

Yes. E84.0 is a billable/specific code that can be used to indicate a diagnosis for reimbursement purposes.

What category does E84.0 belong to?

It belongs to category E84 – Cystic fibrosis.

Source: CDC/NCHS ICD-10-CM FY2027 code files, tabular list and index. Reference only – code assignment must follow the official ICD-10-CM guidelines and documentation in the medical record.