E83.821 – ENPP1 deficiency causing generalized arterial calcification of infancy

ICD-10-CM 2027 diagnosis code · Metabolic disorders

Billable code

ICD-10-CM code E83.821
Code
E83.821 (claims format: E83821)
Description
ENPP1 deficiency causing generalized arterial calcification of infancy
Short description
ENPP1 deficiency causing gen arterial calcifcn of infancy
Billable
Yes – valid for HIPAA-covered transactions
Valid for
Dates of service October 1, 2026 – September 30, 2027 (FY2027)
Chapter
4. Endocrine, nutritional and metabolic diseases (E00-E89)
Block
E70-E88 Metabolic disorders
Parent codes
E83 › E83.8 › E83.82

Notes for E83.821

Code also:
  • , if applicable, associated conditions such as:
  • heart failure (I50.-)
  • other secondary hypertension (I15.8)

Notes inherited from parent codes

Instructional notes at a category or block level apply to every code below it.

E83 – Disorders of mineral metabolism

Excludes1 (not coded here):
  • dietary mineral deficiency (E58-E61)
  • parathyroid disorders (E20-E21)
  • vitamin D deficiency (E55.-)

Block E70-E88

Excludes1 (not coded here):
  • androgen insensitivity syndrome (E34.5-)
  • congenital adrenal hyperplasia (E25.0)
  • hemolytic anemias attributable to enzyme disorders (D55.-)
  • Marfan syndrome (Q87.4-)
  • 5-alpha-reductase deficiency (E29.1)
Excludes2 (not included here):
  • Ehlers-Danlos syndromes (Q79.6-)

Index terms for E83.821

Entries in the ICD-10-CM alphabetic index that lead to this code:

Related codes in E83.82

Frequently asked questions

What is ICD-10 code E83.821?

E83.821 is the ICD-10-CM code for eNPP1 deficiency causing generalized arterial calcification of infancy, in the block E70-E88 (Metabolic disorders).

Is E83.821 a billable code?

Yes. E83.821 is a billable/specific code that can be used to indicate a diagnosis for reimbursement purposes.

What category does E83.821 belong to?

It belongs to category E83 – Disorders of mineral metabolism.

Source: CDC/NCHS ICD-10-CM FY2027 code files, tabular list and index. Reference only – code assignment must follow the official ICD-10-CM guidelines and documentation in the medical record.