E75.00 – GM2 gangliosidosis, unspecified

ICD-10-CM 2027 diagnosis code · Metabolic disorders

Billable code

ICD-10-CM code E75.00

Code: E75.00 (claims format: E7500)
Description: GM2 gangliosidosis, unspecified
Billable: Yes – valid for HIPAA-covered transactions
Valid for: Dates of service October 1, 2026 – September 30, 2027 (FY2027)
Chapter: 4. Endocrine, nutritional and metabolic diseases (E00-E89)
Block: E70-E88 Metabolic disorders
Parent codes: E75 › E75.0

Notes inherited from parent codes

Instructional notes at a category or block level apply to every code below it.

E75 – Disorders of sphingolipid metabolism and other lipid storage disorders

Excludes1 (not coded here):

mucolipidosis, types I-III (E77.0-E77.1)
Refsum's disease (G60.1)

Block E70-E88

Excludes1 (not coded here):

androgen insensitivity syndrome (E34.5-)
congenital adrenal hyperplasia (E25.0)
hemolytic anemias attributable to enzyme disorders (D55.-)
Marfan syndrome (Q87.4-)
5-alpha-reductase deficiency (E29.1)

Excludes2 (not included here):

Ehlers-Danlos syndromes (Q79.6-)

Index terms for E75.00

Entries in the ICD-10-CM alphabetic index that lead to this code:

Gangliosidosis, GM2

Related codes in E75.0

E75.01 – Sandhoff diseaseBillable
E75.02 – Tay-Sachs diseaseBillable
E75.09 – Other GM2 gangliosidosisBillable

Frequently asked questions

What is ICD-10 code E75.00?

E75.00 is the ICD-10-CM code for gM2 gangliosidosis, unspecified, in the block E70-E88 (Metabolic disorders).

Is E75.00 a billable code?

Yes. E75.00 is a billable/specific code that can be used to indicate a diagnosis for reimbursement purposes.

What category does E75.00 belong to?

It belongs to category E75 – Disorders of sphingolipid metabolism and other lipid storage disorders.

Source: CDC/NCHS ICD-10-CM FY2027 code files, tabular list and index. Reference only – code assignment must follow the official ICD-10-CM guidelines and documentation in the medical record.