E75 – Disorders of sphingolipid metabolism and other lipid storage disorders

ICD-10-CM 2027 diagnosis code · Metabolic disorders

Non-billable header

ICD-10-CM code E75

Code: E75 (claims format: E75)
Description: Disorders of sphingolipid metabolism and other lipid storage disorders
Short description: Disord of sphingolipid metab and oth lipid storage disorders
Billable: No – use a more specific code below
Valid for: Dates of service October 1, 2026 – September 30, 2027 (FY2027)
Chapter: 4. Endocrine, nutritional and metabolic diseases (E00-E89)
Block: E70-E88 Metabolic disorders

Billable codes under E75

E75 is a header code and cannot be used on claims. Choose the most specific code:

E75.0 – GM2 gangliosidosisHeader (more codes below)
E75.1 – Other and unspecified gangliosidosisHeader (more codes below)
E75.2 – Other sphingolipidosisHeader (more codes below)
E75.3 – Sphingolipidosis, unspecifiedBillable
E75.4 – Neuronal ceroid lipofuscinosisBillable
E75.5 – Other lipid storage disordersBillable
E75.6 – Lipid storage disorder, unspecifiedBillable

Notes for E75

Excludes1 (not coded here):

mucolipidosis, types I-III (E77.0-E77.1)
Refsum's disease (G60.1)

Notes inherited from parent codes

Instructional notes at a category or block level apply to every code below it.

Block E70-E88

Excludes1 (not coded here):

androgen insensitivity syndrome (E34.5-)
congenital adrenal hyperplasia (E25.0)
hemolytic anemias attributable to enzyme disorders (D55.-)
Marfan syndrome (Q87.4-)
5-alpha-reductase deficiency (E29.1)

Excludes2 (not included here):

Ehlers-Danlos syndromes (Q79.6-)

Index terms for E75

Entries in the ICD-10-CM alphabetic index that lead to this code:

Frequently asked questions

What is ICD-10 code E75?

E75 is the ICD-10-CM code for disorders of sphingolipid metabolism and other lipid storage disorders, in the block E70-E88 (Metabolic disorders).

Is E75 a billable code?

No. E75 is a header code with more specific child codes; report one of the billable codes listed above.

Source: CDC/NCHS ICD-10-CM FY2027 code files, tabular list and index. Reference only – code assignment must follow the official ICD-10-CM guidelines and documentation in the medical record.