E71.511 – Neonatal adrenoleukodystrophy

ICD-10-CM 2027 diagnosis code · Metabolic disorders

Billable code

ICD-10-CM code E71.511
Code
E71.511 (claims format: E71511)
Description
Neonatal adrenoleukodystrophy
Billable
Yes – valid for HIPAA-covered transactions
Valid for
Dates of service October 1, 2026 – September 30, 2027 (FY2027)
Chapter
4. Endocrine, nutritional and metabolic diseases (E00-E89)
Block
E70-E88 Metabolic disorders
Parent codes
E71 › E71.5 › E71.51

Notes for E71.511

Excludes1 (not coded here):
  • X-linked adrenoleukodystrophy (E71.42-)

Notes inherited from parent codes

Instructional notes at a category or block level apply to every code below it.

E71.5 – Peroxisomal disorders

Excludes1 (not coded here):
  • Schilder's disease (G37.0)

E71.51 – Disorders of peroxisome biogenesis

Applicable to:
  • Group 1 peroxisomal disorders
Excludes1 (not coded here):

Block E70-E88

Excludes1 (not coded here):
  • androgen insensitivity syndrome (E34.5-)
  • congenital adrenal hyperplasia (E25.0)
  • hemolytic anemias attributable to enzyme disorders (D55.-)
  • Marfan syndrome (Q87.4-)
  • 5-alpha-reductase deficiency (E29.1)
Excludes2 (not included here):
  • Ehlers-Danlos syndromes (Q79.6-)

Index terms for E71.511

Entries in the ICD-10-CM alphabetic index that lead to this code:

Related codes in E71.51

Frequently asked questions

What is ICD-10 code E71.511?

E71.511 is the ICD-10-CM code for neonatal adrenoleukodystrophy, in the block E70-E88 (Metabolic disorders).

Is E71.511 a billable code?

Yes. E71.511 is a billable/specific code that can be used to indicate a diagnosis for reimbursement purposes.

What category does E71.511 belong to?

It belongs to category E71 – Disorders of branched-chain amino-acid metabolism and fatty-acid metabolism.

Source: CDC/NCHS ICD-10-CM FY2027 code files, tabular list and index. Reference only – code assignment must follow the official ICD-10-CM guidelines and documentation in the medical record.