E71.5 – Peroxisomal disorders

ICD-10-CM 2027 diagnosis code · Metabolic disorders

Non-billable header

ICD-10-CM code E71.5

Code: E71.5 (claims format: E715)
Description: Peroxisomal disorders
Billable: No – use a more specific code below
Valid for: Dates of service October 1, 2026 – September 30, 2027 (FY2027)
Chapter: 4. Endocrine, nutritional and metabolic diseases (E00-E89)
Block: E70-E88 Metabolic disorders
Parent codes: E71

Billable codes under E71.5

E71.5 is a header code and cannot be used on claims. Choose the most specific code:

E71.50 – Peroxisomal disorder, unspecifiedBillable
E71.51 – Disorders of peroxisome biogenesisHeader (more codes below)
E71.52 – X-linked adrenoleukodystrophyHeader (more codes below)
E71.53 – Other group 2 peroxisomal disordersBillable
E71.54 – Other peroxisomal disordersHeader (more codes below)

Notes for E71.5

Excludes1 (not coded here):

Schilder's disease (G37.0)

Notes inherited from parent codes

Instructional notes at a category or block level apply to every code below it.

Block E70-E88

Excludes1 (not coded here):

androgen insensitivity syndrome (E34.5-)
congenital adrenal hyperplasia (E25.0)
hemolytic anemias attributable to enzyme disorders (D55.-)
Marfan syndrome (Q87.4-)
5-alpha-reductase deficiency (E29.1)

Excludes2 (not included here):

Ehlers-Danlos syndromes (Q79.6-)

Index terms for E71.5

Entries in the ICD-10-CM alphabetic index that lead to this code:

Aciduria, glutaric, type III

Related codes in E71

Frequently asked questions

What is ICD-10 code E71.5?

E71.5 is the ICD-10-CM code for peroxisomal disorders, in the block E70-E88 (Metabolic disorders).

Is E71.5 a billable code?

No. E71.5 is a header code with more specific child codes; report one of the billable codes listed above.

What category does E71.5 belong to?

It belongs to category E71 – Disorders of branched-chain amino-acid metabolism and fatty-acid metabolism.

Source: CDC/NCHS ICD-10-CM FY2027 code files, tabular list and index. Reference only – code assignment must follow the official ICD-10-CM guidelines and documentation in the medical record.