E71.4 – Disorders of carnitine metabolism
ICD-10-CM 2027 diagnosis code · Metabolic disorders
ICD-10-CM code
E71.4
- Code
E71.4(claims format:E714)- Description
- Disorders of carnitine metabolism
- Billable
- No – use a more specific code below
- Valid for
- Dates of service October 1, 2026 – September 30, 2027 (FY2027)
- Chapter
- 4. Endocrine, nutritional and metabolic diseases (E00-E89)
- Block
- E70-E88 Metabolic disorders
- Parent codes
- E71
Billable codes under E71.4
E71.4 is a header code and cannot be used on claims. Choose the most specific code:
- E71.40 – Disorder of carnitine metabolism, unspecifiedBillable
- E71.41 – Primary carnitine deficiencyBillable
- E71.42 – Carnitine deficiency due to inborn errors of metabolismBillable
- E71.43 – Iatrogenic carnitine deficiencyBillable
- E71.44 – Other secondary carnitine deficiencyHeader (more codes below)
Notes for E71.4
Excludes1 (not coded here):
- Muscle carnitine palmitoyltransferase deficiency (E71.314)
Notes inherited from parent codes
Instructional notes at a category or block level apply to every code below it.
Block E70-E88
Excludes1 (not coded here):
Excludes2 (not included here):
- Ehlers-Danlos syndromes (Q79.6-)
Related codes in E71
Frequently asked questions
What is ICD-10 code E71.4?
E71.4 is the ICD-10-CM code for disorders of carnitine metabolism, in the block E70-E88 (Metabolic disorders).
Is E71.4 a billable code?
No. E71.4 is a header code with more specific child codes; report one of the billable codes listed above.
What category does E71.4 belong to?
It belongs to category E71 – Disorders of branched-chain amino-acid metabolism and fatty-acid metabolism.
Source: CDC/NCHS ICD-10-CM FY2027 code files, tabular list and index. Reference only – code assignment must follow the official ICD-10-CM guidelines and documentation in the medical record.