E71.313 – Glutaric aciduria type II

ICD-10-CM 2027 diagnosis code · Metabolic disorders

Billable code

ICD-10-CM code E71.313
Code
E71.313 (claims format: E71313)
Description
Glutaric aciduria type II
Billable
Yes – valid for HIPAA-covered transactions
Valid for
Dates of service October 1, 2026 – September 30, 2027 (FY2027)
Chapter
4. Endocrine, nutritional and metabolic diseases (E00-E89)
Block
E70-E88 Metabolic disorders
Parent codes
E71 › E71.3 › E71.31

Notes for E71.313

Applicable to:
  • Glutaric aciduria type II A
  • Glutaric aciduria type II B
  • Glutaric aciduria type II C
Excludes1 (not coded here):
  • glutaric aciduria (type 1) NOS (E72.3)

Notes inherited from parent codes

Instructional notes at a category or block level apply to every code below it.

E71.3 – Disorders of fatty-acid metabolism

Excludes1 (not coded here):
  • peroxisomal disorders (E71.5)
  • Refsum's disease (G60.1)
  • Schilder's disease (G37.0)
Excludes2 (not included here):
  • carnitine deficiency due to inborn error of metabolism (E71.42)

Block E70-E88

Excludes1 (not coded here):
  • androgen insensitivity syndrome (E34.5-)
  • congenital adrenal hyperplasia (E25.0)
  • hemolytic anemias attributable to enzyme disorders (D55.-)
  • Marfan syndrome (Q87.4-)
  • 5-alpha-reductase deficiency (E29.1)
Excludes2 (not included here):
  • Ehlers-Danlos syndromes (Q79.6-)

Index terms for E71.313

Entries in the ICD-10-CM alphabetic index that lead to this code:

Related codes in E71.31

Frequently asked questions

What is ICD-10 code E71.313?

E71.313 is the ICD-10-CM code for glutaric aciduria type II, in the block E70-E88 (Metabolic disorders).

Is E71.313 a billable code?

Yes. E71.313 is a billable/specific code that can be used to indicate a diagnosis for reimbursement purposes.

What category does E71.313 belong to?

It belongs to category E71 – Disorders of branched-chain amino-acid metabolism and fatty-acid metabolism.

Source: CDC/NCHS ICD-10-CM FY2027 code files, tabular list and index. Reference only – code assignment must follow the official ICD-10-CM guidelines and documentation in the medical record.