D68.1 – Hereditary factor XI deficiency

ICD-10-CM 2027 diagnosis code · Coagulation defects, purpura and other hemorrhagic conditions

Billable code

ICD-10-CM code D68.1

Code: D68.1 (claims format: D681)
Description: Hereditary factor XI deficiency
Billable: Yes – valid for HIPAA-covered transactions
Valid for: Dates of service October 1, 2026 – September 30, 2027 (FY2027)
Chapter: 3. Diseases of the blood and blood-forming organs and certain disorders involving the immune mechanism (D50-D89)
Block: D65-D69 Coagulation defects, purpura and other hemorrhagic conditions
Parent codes: D68

Notes for D68.1

Applicable to:

Hemophilia C
Plasma thromboplastin antecedent [PTA] deficiency
Rosenthal's disease

Notes inherited from parent codes

Instructional notes at a category or block level apply to every code below it.

D68 – Other coagulation defects

Excludes1 (not coded here):

abnormal coagulation profile NOS (R79.1)

Excludes2 (not included here):

coagulation defects complicating abortion or ectopic or molar pregnancy (O00-O07, O08.1)
coagulation defects complicating pregnancy, childbirth and the puerperium (O45.0, O46.0, O67.0, O72.3)

Index terms for D68.1

Entries in the ICD-10-CM alphabetic index that lead to this code:

Related codes in D68

D68.0 – Von Willebrand diseaseHeader
D68.2 – Hereditary deficiency of other clotting factorsBillable
D68.3 – Hemorrhagic disorder due to circulating anticoagulantsHeader
D68.4 – Acquired coagulation factor deficiencyBillable
D68.5 – Primary thrombophiliaHeader
D68.6 – Other thrombophiliaHeader
D68.8 – Other specified coagulation defectsBillable
D68.9 – Coagulation defect, unspecifiedBillable

Frequently asked questions

What is ICD-10 code D68.1?

D68.1 is the ICD-10-CM code for hereditary factor XI deficiency, in the block D65-D69 (Coagulation defects, purpura and other hemorrhagic conditions).

Is D68.1 a billable code?

Yes. D68.1 is a billable/specific code that can be used to indicate a diagnosis for reimbursement purposes.

What category does D68.1 belong to?

It belongs to category D68 – Other coagulation defects.

Source: CDC/NCHS ICD-10-CM FY2027 code files, tabular list and index. Reference only – code assignment must follow the official ICD-10-CM guidelines and documentation in the medical record.