D68.0 – Von Willebrand disease

ICD-10-CM 2027 diagnosis code · Coagulation defects, purpura and other hemorrhagic conditions

Non-billable header

ICD-10-CM code D68.0

Code: D68.0 (claims format: D680)
Description: Von Willebrand disease
Billable: No – use a more specific code below
Valid for: Dates of service October 1, 2026 – September 30, 2027 (FY2027)
Chapter: 3. Diseases of the blood and blood-forming organs and certain disorders involving the immune mechanism (D50-D89)
Block: D65-D69 Coagulation defects, purpura and other hemorrhagic conditions
Parent codes: D68

Billable codes under D68.0

D68.0 is a header code and cannot be used on claims. Choose the most specific code:

D68.00 – Von Willebrand disease, unspecifiedBillable
D68.01 – Von Willebrand disease, type 1Billable
D68.02 – Von Willebrand disease, type 2Header (more codes below)
D68.03 – Von Willebrand disease, type 3Billable
D68.04 – Acquired von Willebrand diseaseBillable
D68.09 – Other von Willebrand diseaseBillable

Notes for D68.0

Excludes1 (not coded here):

capillary fragility (hereditary) (D69.8)
factor VIII deficiency NOS (D66)
factor VIII deficiency with functional defect (D66)

Notes inherited from parent codes

Instructional notes at a category or block level apply to every code below it.

D68 – Other coagulation defects

Excludes1 (not coded here):

abnormal coagulation profile NOS (R79.1)

Excludes2 (not included here):

coagulation defects complicating abortion or ectopic or molar pregnancy (O00-O07, O08.1)
coagulation defects complicating pregnancy, childbirth and the puerperium (O45.0, O46.0, O67.0, O72.3)

Related codes in D68

D68.1 – Hereditary factor XI deficiencyBillable
D68.2 – Hereditary deficiency of other clotting factorsBillable
D68.3 – Hemorrhagic disorder due to circulating anticoagulantsHeader
D68.4 – Acquired coagulation factor deficiencyBillable
D68.5 – Primary thrombophiliaHeader
D68.6 – Other thrombophiliaHeader
D68.8 – Other specified coagulation defectsBillable
D68.9 – Coagulation defect, unspecifiedBillable

Frequently asked questions

What is ICD-10 code D68.0?

D68.0 is the ICD-10-CM code for von Willebrand disease, in the block D65-D69 (Coagulation defects, purpura and other hemorrhagic conditions).

Is D68.0 a billable code?

No. D68.0 is a header code with more specific child codes; report one of the billable codes listed above.

What category does D68.0 belong to?

It belongs to category D68 – Other coagulation defects.

Source: CDC/NCHS ICD-10-CM FY2027 code files, tabular list and index. Reference only – code assignment must follow the official ICD-10-CM guidelines and documentation in the medical record.