D68.01 – Von Willebrand disease, type 1

ICD-10-CM 2027 diagnosis code · Coagulation defects, purpura and other hemorrhagic conditions

Billable code

ICD-10-CM code D68.01

Code: D68.01 (claims format: D6801)
Description: Von Willebrand disease, type 1
Billable: Yes – valid for HIPAA-covered transactions
Valid for: Dates of service October 1, 2026 – September 30, 2027 (FY2027)
Chapter: 3. Diseases of the blood and blood-forming organs and certain disorders involving the immune mechanism (D50-D89)
Block: D65-D69 Coagulation defects, purpura and other hemorrhagic conditions
Parent codes: D68 › D68.0

Notes for D68.01

Applicable to:

Partial quantitative deficiency of von Willebrand factor
Type 1C von Willebrand disease

Notes inherited from parent codes

Instructional notes at a category or block level apply to every code below it.

D68 – Other coagulation defects

Excludes1 (not coded here):

abnormal coagulation profile NOS (R79.1)

Excludes2 (not included here):

coagulation defects complicating abortion or ectopic or molar pregnancy (O00-O07, O08.1)
coagulation defects complicating pregnancy, childbirth and the puerperium (O45.0, O46.0, O67.0, O72.3)

D68.0 – Von Willebrand disease

Excludes1 (not coded here):

capillary fragility (hereditary) (D69.8)
factor VIII deficiency NOS (D66)
factor VIII deficiency with functional defect (D66)

Index terms for D68.01

Entries in the ICD-10-CM alphabetic index that lead to this code:

Related codes in D68.0

D68.00 – Von Willebrand disease, unspecifiedBillable
D68.02 – Von Willebrand disease, type 2Header
D68.03 – Von Willebrand disease, type 3Billable
D68.04 – Acquired von Willebrand diseaseBillable
D68.09 – Other von Willebrand diseaseBillable

Frequently asked questions

What is ICD-10 code D68.01?

D68.01 is the ICD-10-CM code for von Willebrand disease, type 1, in the block D65-D69 (Coagulation defects, purpura and other hemorrhagic conditions).

Is D68.01 a billable code?

Yes. D68.01 is a billable/specific code that can be used to indicate a diagnosis for reimbursement purposes.

What category does D68.01 belong to?

It belongs to category D68 – Other coagulation defects.

Source: CDC/NCHS ICD-10-CM FY2027 code files, tabular list and index. Reference only – code assignment must follow the official ICD-10-CM guidelines and documentation in the medical record.