Q07.0 – Arnold-Chiari syndrome

ICD-10-CM 2027 diagnosis code · Congenital malformations of the nervous system

Non-billable header

ICD-10-CM code Q07.0

Code: Q07.0 (claims format: Q070)
Description: Arnold-Chiari syndrome
Billable: No – use a more specific code below
Valid for: Dates of service October 1, 2026 – September 30, 2027 (FY2027)
Chapter: 17. Congenital malformations, deformations, chromosomal abnormalities, and genetic disorders (Q00-QA1)
Block: Q00-Q07 Congenital malformations of the nervous system
Parent codes: Q07

Billable codes under Q07.0

Q07.0 is a header code and cannot be used on claims. Choose the most specific code:

Notes for Q07.0

Applicable to:

Arnold-Chiari syndrome, type II

Excludes1 (not coded here):

Arnold-Chiari syndrome, type III (Q01.-)
Arnold-Chiari syndrome, type IV (Q04.8)

Notes inherited from parent codes

Instructional notes at a category or block level apply to every code below it.

Q07 – Other congenital malformations of nervous system

Excludes2 (not included here):

congenital central alveolar hypoventilation syndrome (G47.35)
familial dysautonomia [Riley-Day] (G90.1)
neurofibromatosis (nonmalignant) (Q85.0-)

Related codes in Q07

Frequently asked questions

What is ICD-10 code Q07.0?

Q07.0 is the ICD-10-CM code for arnold-Chiari syndrome, in the block Q00-Q07 (Congenital malformations of the nervous system).

Is Q07.0 a billable code?

No. Q07.0 is a header code with more specific child codes; report one of the billable codes listed above.

What category does Q07.0 belong to?

It belongs to category Q07 – Other congenital malformations of nervous system.

Source: CDC/NCHS ICD-10-CM FY2027 code files, tabular list and index. Reference only – code assignment must follow the official ICD-10-CM guidelines and documentation in the medical record.