Q00 – Anencephaly and similar malformations
ICD-10-CM 2027 diagnosis code · Congenital malformations of the nervous system
ICD-10-CM code
Q00
- Code
Q00(claims format:Q00)- Description
- Anencephaly and similar malformations
- Billable
- No – use a more specific code below
- Valid for
- Dates of service October 1, 2026 – September 30, 2027 (FY2027)
- Chapter
- 17. Congenital malformations, deformations, chromosomal abnormalities, and genetic disorders (Q00-QA1)
- Block
- Q00-Q07 Congenital malformations of the nervous system
Billable codes under Q00
Q00 is a header code and cannot be used on claims. Choose the most specific code:
- Q00.0 – AnencephalyBillable
- Q00.1 – CraniorachischisisBillable
- Q00.2 – IniencephalyBillable
Frequently asked questions
What is ICD-10 code Q00?
Q00 is the ICD-10-CM code for anencephaly and similar malformations, in the block Q00-Q07 (Congenital malformations of the nervous system).
Is Q00 a billable code?
No. Q00 is a header code with more specific child codes; report one of the billable codes listed above.
Source: CDC/NCHS ICD-10-CM FY2027 code files, tabular list and index. Reference only – code assignment must follow the official ICD-10-CM guidelines and documentation in the medical record.