E71.19 – Other disorders of branched-chain amino-acid metabolism
ICD-10-CM 2027 diagnosis code · Metabolic disorders
ICD-10-CM code
E71.19
- Code
E71.19(claims format:E7119)- Description
- Other disorders of branched-chain amino-acid metabolism
- Billable
- Yes – valid for HIPAA-covered transactions
- Valid for
- Dates of service October 1, 2026 – September 30, 2027 (FY2027)
- Chapter
- 4. Endocrine, nutritional and metabolic diseases (E00-E89)
- Block
- E70-E88 Metabolic disorders
- Parent codes
- E71 › E71.1
Notes for E71.19
Applicable to:
- Hyperleucine-isoleucinemia
- Hypervalinemia
Notes inherited from parent codes
Instructional notes at a category or block level apply to every code below it.
Block E70-E88
Excludes1 (not coded here):
Excludes2 (not included here):
- Ehlers-Danlos syndromes (Q79.6-)
Index terms for E71.19
Entries in the ICD-10-CM alphabetic index that lead to this code:
- Isoleucinosis
- Hypervalinemia
- Disorder, hypervalinemia
- Hyperleucine-isoleucinemia
- Hypoglycemia, leucine-induced
- Disorder, metabolism NOS, valine
- Disorder, metabolism NOS, leucine
- Disorder, hyperleucine-isoleucinemia
- Disorder, metabolism NOS, isoleucine
- Disorder, branched-chain amino-acid metabolism, specified NEC
- Disorder, metabolism NOS, amino-acid, branched chain, hypervalinemia
- Disorder, metabolism NOS, amino-acid, branched chain, other specified
- Disorder, metabolism NOS, amino-acid, branched chain, hyperleucine-isoleucinemia
Related codes in E71.1
Frequently asked questions
What is ICD-10 code E71.19?
E71.19 is the ICD-10-CM code for other disorders of branched-chain amino-acid metabolism, in the block E70-E88 (Metabolic disorders).
Is E71.19 a billable code?
Yes. E71.19 is a billable/specific code that can be used to indicate a diagnosis for reimbursement purposes.
What category does E71.19 belong to?
It belongs to category E71 – Disorders of branched-chain amino-acid metabolism and fatty-acid metabolism.
Source: CDC/NCHS ICD-10-CM FY2027 code files, tabular list and index. Reference only – code assignment must follow the official ICD-10-CM guidelines and documentation in the medical record.