E71.110 – Isovaleric acidemia

ICD-10-CM 2027 diagnosis code · Metabolic disorders

Billable code

ICD-10-CM code E71.110
Code
E71.110 (claims format: E71110)
Description
Isovaleric acidemia
Billable
Yes – valid for HIPAA-covered transactions
Valid for
Dates of service October 1, 2026 – September 30, 2027 (FY2027)
Chapter
4. Endocrine, nutritional and metabolic diseases (E00-E89)
Block
E70-E88 Metabolic disorders
Parent codes
E71 › E71.1 › E71.11

Notes inherited from parent codes

Instructional notes at a category or block level apply to every code below it.

Block E70-E88

Excludes1 (not coded here):
  • androgen insensitivity syndrome (E34.5-)
  • congenital adrenal hyperplasia (E25.0)
  • hemolytic anemias attributable to enzyme disorders (D55.-)
  • Marfan syndrome (Q87.4-)
  • 5-alpha-reductase deficiency (E29.1)
Excludes2 (not included here):
  • Ehlers-Danlos syndromes (Q79.6-)

Index terms for E71.110

Entries in the ICD-10-CM alphabetic index that lead to this code:

Related codes in E71.11

Frequently asked questions

What is ICD-10 code E71.110?

E71.110 is the ICD-10-CM code for isovaleric acidemia, in the block E70-E88 (Metabolic disorders).

Is E71.110 a billable code?

Yes. E71.110 is a billable/specific code that can be used to indicate a diagnosis for reimbursement purposes.

What category does E71.110 belong to?

It belongs to category E71 – Disorders of branched-chain amino-acid metabolism and fatty-acid metabolism.

Source: CDC/NCHS ICD-10-CM FY2027 code files, tabular list and index. Reference only – code assignment must follow the official ICD-10-CM guidelines and documentation in the medical record.