E70.0 – Classical phenylketonuria
ICD-10-CM 2027 diagnosis code · Metabolic disorders
ICD-10-CM code
E70.0
- Code
E70.0(claims format:E700)- Description
- Classical phenylketonuria
- Billable
- Yes – valid for HIPAA-covered transactions
- Valid for
- Dates of service October 1, 2026 – September 30, 2027 (FY2027)
- Chapter
- 4. Endocrine, nutritional and metabolic diseases (E00-E89)
- Block
- E70-E88 Metabolic disorders
- Parent codes
- E70
Notes inherited from parent codes
Instructional notes at a category or block level apply to every code below it.
Block E70-E88
Excludes1 (not coded here):
Excludes2 (not included here):
- Ehlers-Danlos syndromes (Q79.6-)
Index terms for E70.0
Entries in the ICD-10-CM alphabetic index that lead to this code:
Related codes in E70
- E70.1 – Other hyperphenylalaninemiasBillable
- E70.2 – Disorders of tyrosine metabolismHeader
- E70.3 – AlbinismHeader
- E70.4 – Disorders of histidine metabolismHeader
- E70.5 – Disorders of tryptophan metabolismBillable
- E70.8 – Other disorders of aromatic amino-acid metabolismHeader
- E70.9 – Disorder of aromatic amino-acid metabolism, unspecifiedBillable
Frequently asked questions
What is ICD-10 code E70.0?
E70.0 is the ICD-10-CM code for classical phenylketonuria, in the block E70-E88 (Metabolic disorders).
Is E70.0 a billable code?
Yes. E70.0 is a billable/specific code that can be used to indicate a diagnosis for reimbursement purposes.
What category does E70.0 belong to?
It belongs to category E70 – Disorders of aromatic amino-acid metabolism.
Source: CDC/NCHS ICD-10-CM FY2027 code files, tabular list and index. Reference only – code assignment must follow the official ICD-10-CM guidelines and documentation in the medical record.