ICD-10 Code for Dystrophy

The ICD-10-CM 2027 alphabetic index lists dystrophy, dystrophia with the subterms below. More specific codes depend on the details documented, as listed in the official index (48 codes, 41 billable).

Index entries for Dystrophy

adiposogenital – E23.6
autosomal recessive, childhood type, muscular dystrophy resembling Duchenne or Becker – G71.01
Becker's type – G71.01
cervical sympathetic – G90.2
choroid (hereditary) – H31.20
- central areolar – H31.22
- choroideremia – H31.21
- gyrate atrophy – H31.23
- specified type NEC – H31.29
cornea (hereditary) – H18.50- (header)
- endothelial – H18.51- (header)
- epithelial – H18.52- (header)
- granular – H18.53- (header)
- lattice – H18.54- (header)
- macular – H18.55- (header)
- specified type NEC – H18.59- (header)
Duchenne's type – G71.01
due to malnutrition – E45
Erb's – G71.02
Fuchs' – H18.51- (header)
Gower's muscular – G71.01
hair – L67.8
infantile neuraxonal – G31.89
Landouzy-Déjérine – G71.02
Leyden-Möbius – G71.039 – see also Dystrophy, muscular, limb-girdle, by type
- meaning Limb girdle muscular dystrophy NOS – G71.039
- meaning Limb girdle muscular dystrophy, other specified type, – see by type
- meaning Limb girdle muscular dystrophy, specified type NEC – G71.038
- meaning Limb girdle muscular dystrophy type 2A (autosomal recessive) – G71.032
muscular – G71.00
- autosomal recessive, childhood type, muscular dystrophy resembling Duchenne or Becker – G71.01
- benign (Becker type) – G71.01
  - scapuloperoneal with early contractures [Emery-Dreifuss] – G71.09
- congenital (hereditary) (progressive) (with specific morphological abnormalities of the muscle fiber) – G71.09
  - myotonic – G71.11
- distal – G71.09
- Duchenne type – G71.01
- Emery-Dreifuss – G71.09
- Erb type – G71.02
- facioscapulohumeral – G71.02
- Gower's – G71.01
- hereditary (progressive) – G71.09 – see also Dystrophy, muscular, by type
- Landouzy-Déjérine type – G71.02
- limb-girdle – G71.039
  - alpha-sarcoglycan-related – G71.0341
  - anoctamin-5-related autosomal recessive (R12) – G71.035
  - autosomal recessive NEC – G71.038
  - beta-sarcoglycan-related – G71.0342
  - calpain-3-related – G71.032
    - autosomal dominant – G71.031
    - autosomal recessive – G71.032
  - collagen VI related
    - autosomal dominant – G71.031
    - autosomal recessive – G71.038
  - D1 (autosomal dominant) – G71.031
  - D2 (autosomal dominant) – G71.031
  - D3 (autosomal dominant) – G71.031
  - D4 (autosomal dominant) – G71.031
  - D5 (autosomal dominant) – G71.031
  - delta-sarcoglycan-related – G71.0349
  - due to
    - alpha sarcoglycan dysfunction – G71.0341
    - anoctamin-5 dysfunction – G71.035
    - beta sarcoglycan dysfunction – G71.0342
    - fukutin related protein dysfunction – G71.036
    - sarcoglycan dysfunction, specified NEC – G71.0349
  - FKRP-related autosomal recessive – G71.038
  - gamma-sarcoglycan-related – G71.0349
  - R1 (autosomal recessive) – G71.032
  - R2 (autosomal recessive) – G71.033
  - R3 (autosomal recessive) – G71.0341
  - R4 (autosomal recessive) – G71.0342
  - R5 (autosomal recessive) – G71.0349
  - R6 (autosomal recessive) – G71.0349
  - R7 (autosomal recessive) – G71.038
  - R8 (autosomal recessive) – G71.038
  - R9 (autosomal recessive) – G71.036
  - R10 (autosomal recessive) – G71.038
  - R11 (autosomal recessive) – G71.038
  - R12 (autosomal recessive) – G71.035
  - R13 (autosomal recessive) – G71.038
  - R14 (autosomal recessive) – G71.038
  - R15 (autosomal recessive) – G71.038
  - R16 (autosomal recessive) – G71.038
  - R17 (autosomal recessive) – G71.038
  - R18 (autosomal recessive) – G71.038
  - R19 (autosomal recessive) – G71.038
  - R20 (autosomal recessive) – G71.038
  - R21 (autosomal recessive) – G71.038
  - R22 (autosomal recessive) – G71.038
  - R23 (autosomal recessive) – G71.038
  - R24 (autosomal recessive) – G71.038
  - type 1 (autosomal dominant) – G71.031
  - type 1A (autosomal dominant) – G71.031
  - type 1B (autosomal dominant) – G71.031
  - type 1C (autosomal dominant) – G71.031
  - type 1E (autosomal dominant) – G71.031
  - type 1H (autosomal dominant) – G71.031
  - type 1I (autosomal dominant) – G71.031
  - type 2 (autosomal recessive) – G71.038
    - specified NEC – G71.038
  - type 2A (autosomal recessive) – G71.032
  - type 2B (autosomal recessive) – G71.033
  - type 2C (autosomal recessive) – G71.0349
  - type 2D (autosomal recessive) – G71.0341
  - type 2E (autosomal recessive) – G71.0342
  - type 2F (autosomal recessive) – G71.0349
  - type 2G (autosomal recessive) – G71.038
  - type 2H (autosomal recessive) – G71.038
  - type 2I (autosomal recessive) – G71.036
  - type 2J (autosomal recessive) – G71.038
  - type 2K (autosomal recessive) – G71.038
  - type 2L (autosomal recessive) – G71.035
  - type 2M (autosomal recessive) – G71.038
  - type 2N (autosomal recessive) – G71.038
  - type 2O (autosomal recessive) – G71.038
  - type 2P (autosomal recessive) – G71.038
  - type 2Q (autosomal recessive) – G71.038
  - type 2S (autosomal recessive) – G71.038
  - type 2T (autosomal recessive) – G71.038
  - type 2U (autosomal recessive) – G71.038
- myotonic – G71.11
- progressive (hereditary) – G71.09 – see also Dystrophy, muscular, by type
  - Charcot-Marie (-Tooth) – G60.0
- pseudohypertrophic (infantile) – G71.01
- scapulohumeral – G71.02
- scapuloperoneal – G71.09
- severe (Duchenne type) – G71.01
- specified type NEC – G71.09
myocardium, myocardial – see Degeneration, myocardial
myotonic, myotonica – G71.11
nail – L60.3
- congenital – Q84.6
nutritional – E45
ocular – G71.09
oculocerebrorenal – E72.03
oculopharyngeal – G71.09
ovarian – N83.8
polyglandular – E31.8
reflex (neuromuscular) (sympathetic) – see Syndrome, pain, complex regional I
retinal (hereditary) – H35.50
- in
  - lipid storage disorders – E75.6 – H36.89 [manifestation]
  - systemic lipidoses – E75.6 – H36.89 [manifestation]
- involving
  - pigment epithelium – H35.54
  - sensory area – H35.53
- pigmentary – H35.52
- vitreoretinal – H35.51
Salzmann's nodular – see Degeneration, cornea, nodular
scapuloperoneal – G71.09
skin NEC – L98.8
sympathetic (reflex) – see Syndrome, pain, complex regional I
- cervical – G90.2
tapetoretinal – H35.54
thoracic, asphyxiating – Q77.2
unguium – L60.3
- congenital – Q84.6
vitreoretinal – H35.51
vulva – N90.4
yellow (liver) – see Failure, hepatic

How to choose the right code

Start with the main term, then pick the indented subterm that matches the documentation (type, cause, site, laterality, episode of care). Always confirm the code in the tabular list: follow its Excludes1/Excludes2, “code first” and “use additional code” notes, and add a 7th character where required.

Source: CDC/NCHS ICD-10-CM FY2027 alphabetic index.