NPI Atlas

ICD-10 Code for Agammaglobulinemia

The default ICD-10-CM 2027 code for agammaglobulinemia (acquired (secondary)) (nonfamilial) is D80.1 – Nonfamilial hypogammaglobulinemia. More specific codes depend on the details documented, as listed in the official index (3 codes, 3 billable).

Main code: D80.1 – Nonfamilial hypogammaglobulinemia
Billable: Yes

Index entries for Agammaglobulinemia

with
- immunoglobulin-bearing B-lymphocytes – D80.1
- lymphopenia – D81.9
autosomal recessive (Swiss type) – D80.0
Bruton's X-linked – D80.0
common variable (CVAgamma) – D80.1
congenital sex-linked – D80.0
hereditary – D80.0
lymphopenic – D81.9
Swiss type (autosomal recessive) – D80.0
X-linked (with growth hormone deficiency) (Bruton) – D80.0

How to choose the right code

Start with the main term, then pick the indented subterm that matches the documentation (type, cause, site, laterality, episode of care). Always confirm the code in the tabular list: follow its Excludes1/Excludes2, “code first” and “use additional code” notes, and add a 7th character where required.

Source: CDC/NCHS ICD-10-CM FY2027 alphabetic index.