Q82.3 – Incontinentia pigmenti

ICD-10-CM 2027 diagnosis code · Other congenital malformations

Billable code

ICD-10-CM code Q82.3

Code: Q82.3 (claims format: Q823)
Description: Incontinentia pigmenti
Billable: Yes – valid for HIPAA-covered transactions
Valid for: Dates of service October 1, 2026 – September 30, 2027 (FY2027)
Chapter: 17. Congenital malformations, deformations, chromosomal abnormalities, and genetic disorders (Q00-QA1)
Block: Q80-Q89 Other congenital malformations
Parent codes: Q82

Notes inherited from parent codes

Instructional notes at a category or block level apply to every code below it.

Q82 – Other congenital malformations of skin

Excludes1 (not coded here):

acrodermatitis enteropathica (E83.2)
congenital erythropoietic porphyria (E80.0)
pilonidal cyst or sinus (L05.-)
Sturge-Weber (-Dimitri) syndrome (Q85.89)

Index terms for Q82.3

Entries in the ICD-10-CM alphabetic index that lead to this code:

Related codes in Q82

Q82.0 – Hereditary lymphedemaBillable
Q82.1 – Xeroderma pigmentosumBillable
Q82.2 – Congenital cutaneous mastocytosisBillable
Q82.4 – Ectodermal dysplasia (anhidrotic)Billable
Q82.5 – Congenital non-neoplastic nevusBillable
Q82.6 – Congenital sacral dimpleBillable
Q82.8 – Other specified congenital malformations of skinBillable
Q82.9 – Congenital malformation of skin, unspecifiedBillable

Frequently asked questions

What is ICD-10 code Q82.3?

Q82.3 is the ICD-10-CM code for incontinentia pigmenti, in the block Q80-Q89 (Other congenital malformations).

Is Q82.3 a billable code?

Yes. Q82.3 is a billable/specific code that can be used to indicate a diagnosis for reimbursement purposes.

What category does Q82.3 belong to?

It belongs to category Q82 – Other congenital malformations of skin.

Source: CDC/NCHS ICD-10-CM FY2027 code files, tabular list and index. Reference only – code assignment must follow the official ICD-10-CM guidelines and documentation in the medical record.