Q56.1 – Male pseudohermaphroditism, not elsewhere classified

ICD-10-CM 2027 diagnosis code · Congenital malformations of genital organs

Billable code

ICD-10-CM code Q56.1

Code: Q56.1 (claims format: Q561)
Description: Male pseudohermaphroditism, not elsewhere classified
Billable: Yes – valid for HIPAA-covered transactions
Valid for: Dates of service October 1, 2026 – September 30, 2027 (FY2027)
Chapter: 17. Congenital malformations, deformations, chromosomal abnormalities, and genetic disorders (Q00-QA1)
Block: Q50-Q56 Congenital malformations of genital organs
Parent codes: Q56

Notes for Q56.1

Applicable to:

46, XY with streak gonads
Male pseudohermaphroditism NOS

Notes inherited from parent codes

Instructional notes at a category or block level apply to every code below it.

Q56 – Indeterminate sex and pseudohermaphroditism

Excludes1 (not coded here):

46,XX true hermaphrodite (Q99.1)
androgen insensitivity syndrome (E34.5-)
chimera 46,XX/46,XY true hermaphrodite (Q99.0)
female pseudohermaphroditism with adrenocortical disorder (E25.-)
pseudohermaphroditism with specified chromosomal anomaly (Q96-Q99)
pure gonadal dysgenesis (Q99.1)

Block Q50-Q56

Excludes1 (not coded here):

androgen insensitivity syndrome (E34.5-)
syndromes associated with anomalies in the number and form of chromosomes (Q90-Q99)

Index terms for Q56.1

Entries in the ICD-10-CM alphabetic index that lead to this code:

Related codes in Q56

Frequently asked questions

What is ICD-10 code Q56.1?

Q56.1 is the ICD-10-CM code for male pseudohermaphroditism, not elsewhere classified, in the block Q50-Q56 (Congenital malformations of genital organs).

Is Q56.1 a billable code?

Yes. Q56.1 is a billable/specific code that can be used to indicate a diagnosis for reimbursement purposes.

What category does Q56.1 belong to?

It belongs to category Q56 – Indeterminate sex and pseudohermaphroditism.

Source: CDC/NCHS ICD-10-CM FY2027 code files, tabular list and index. Reference only – code assignment must follow the official ICD-10-CM guidelines and documentation in the medical record.