Q50.0 – Congenital absence of ovary

ICD-10-CM 2027 diagnosis code · Congenital malformations of genital organs

Non-billable header

ICD-10-CM code Q50.0

Code: Q50.0 (claims format: Q500)
Description: Congenital absence of ovary
Billable: No – use a more specific code below
Valid for: Dates of service October 1, 2026 – September 30, 2027 (FY2027)
Chapter: 17. Congenital malformations, deformations, chromosomal abnormalities, and genetic disorders (Q00-QA1)
Block: Q50-Q56 Congenital malformations of genital organs
Parent codes: Q50

Billable codes under Q50.0

Q50.0 is a header code and cannot be used on claims. Choose the most specific code:

Q50.01 – Congenital absence of ovary, unilateralBillable
Q50.02 – Congenital absence of ovary, bilateralBillable

Notes for Q50.0

Excludes1 (not coded here):

Turner's syndrome (Q96.-)

Notes inherited from parent codes

Instructional notes at a category or block level apply to every code below it.

Block Q50-Q56

Excludes1 (not coded here):

androgen insensitivity syndrome (E34.5-)
syndromes associated with anomalies in the number and form of chromosomes (Q90-Q99)

Related codes in Q50

Q50.1 – Developmental ovarian cystBillable
Q50.2 – Congenital torsion of ovaryBillable
Q50.3 – Other congenital malformations of ovaryHeader
Q50.4 – Embryonic cyst of fallopian tubeBillable
Q50.5 – Embryonic cyst of broad ligamentBillable
Q50.6 – Other congenital malformations of fallopian tube and broad ligamentBillable

Frequently asked questions

What is ICD-10 code Q50.0?

Q50.0 is the ICD-10-CM code for congenital absence of ovary, in the block Q50-Q56 (Congenital malformations of genital organs).

Is Q50.0 a billable code?

No. Q50.0 is a header code with more specific child codes; report one of the billable codes listed above.

What category does Q50.0 belong to?

It belongs to category Q50 – Congenital malformations of ovaries, fallopian tubes and broad ligaments.

Source: CDC/NCHS ICD-10-CM FY2027 code files, tabular list and index. Reference only – code assignment must follow the official ICD-10-CM guidelines and documentation in the medical record.